Department of Dermatology, Shanghai Pudong New Area People's Hospital, Shanghai 201299, China.
Department of Dermatology, Shanghai Pudong New Area People's Hospital, Shanghai 201299, China.
Photodiagnosis Photodyn Ther. 2022 Jun;38:102890. doi: 10.1016/j.pdpdt.2022.102890. Epub 2022 Apr 28.
A case of phakomatosis pigmentovascularis (PPV) type III a with a zosteriform distribution of nevus spilus as the main manifestation was reported. A 41-year-old man was born with a zosteriform distribution of pigmented rash on the left half-body, namely upper limb, shoulder and back. Physical examination revealed light brown pigments in a giant zosteriform distribution on the extensor side of the left upper limb and the left shoulder and back, with scattered brown spots and patches of variant sizes on the surface, which are consistent with the appearance of nevus spilus (NS). A relatively small area of dark red patch occurred on the left anterior shoulder, which showed telangiectasia and fading after pressing. It was consistent with the performance of a port-wine stain (PWS). Dermoscopy showed a clearer appearance and localized fusion of blood vessels and pigmented patch. He has no systemic involvement. The patient was diagnosed with phakomatosis pigmentovascularis type Ⅲa. NS and PWS can be treated with lasers if required.
报告了一例以痣样毳毛血管痣（PPV）IIIa 型为主要表现的病例，其表现为带状疱疹样分布的痣样毳毛。一名 41 岁男性出生时左侧半身（即上肢、肩部和背部）即有带状疱疹样色素疹。体格检查显示，左上肢和左肩部及背部的伸侧有巨大的带状疱疹样分布的浅棕色色素沉着，表面散布着大小不一的棕色斑点和斑块，符合痣样毳毛（NS）的外观。左前肩部有一个相对较小的暗红色斑块，压迫后可见毛细血管扩张和褪色，符合葡萄酒色斑（PWS）的表现。皮肤镜检查显示血管和色素斑块的外观更清晰，且局部融合。患者无全身受累。该患者被诊断为痣样毳毛血管痣 IIIa 型。如果需要，NS 和 PWS 可以通过激光治疗。
