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葡萄酒色斑(鲜红斑痣)、先天性贝克痣、咖啡斑和雀斑:Ia型色素血管性斑痣性错构瘤病——一种新的组合。

Port-wine-stain (nevus flammeus), congenital Becker's nevus, café-au-lait-macule and lentigines: phakomatosis pigmentovascularis type Ia--a new combination.

作者信息

Joshi A, Garg V K, Agrawal S, Agarwalla A, Thakur A

机构信息

Department of Dermatology, B.P. Koirala Institute of Health Sciences, Dharan, Nepal.

出版信息

J Dermatol. 1999 Dec;26(12):834-6. doi: 10.1111/j.1346-8138.1999.tb02103.x.

DOI:10.1111/j.1346-8138.1999.tb02103.x
PMID:10659508
Abstract

A 16-year-old male had brown macules in a geographic pattern with increased terminal hair on the back and dusky red partially blanchable non progressing macules on his left thigh since birth. Clinical diagnoses of Becker's nevus and port-wine-stain were made and confirmed histopathologically. In addition, he had multiple lentigines on the face and trunk and a single café-au-lait-macule on his chest.

摘要

一名16岁男性自出生以来,背部有呈地图状的褐色斑疹,伴有终毛增多,左大腿有暗红色、部分可褪色且无进展的斑疹。临床诊断为贝克痣和葡萄酒色斑,并经组织病理学证实。此外,他面部和躯干有多处雀斑样痣,胸部有一处咖啡斑。

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