Department of Hematology, Nagano Red Cross Hospital, Japan.
Department of Pathology, Nagano Red Cross Hospital, Japan.
Intern Med. 2022 Nov 15;61(22):3425-3429. doi: 10.2169/internalmedicine.9300-21. Epub 2022 Apr 30.
A 58-year-old man presented with painful edema of the extremities, and a diagnosis of eosinophilic fasciitis (EF) was confirmed. He also met the criteria for hypereosinophilic syndrome (HES), but there were no findings suggestive of malignancies or hematologic neoplasms despite a close examination. He was started on steroid therapy but subsequently developed severe liver dysfunction, hemophagocytic lymphohistiocytosis, hepatosplenomegaly, and renal involvement. The diagnosis of peripheral T-cell lymphoma, not otherwise specified was finally established by a bone marrow reexamination and liver biopsy. In cases of eosinophilia, EF, and/or HES, it is important to suspect an intrinsic abnormality, including potential T-cell lymphoma.
一位 58 岁男性因四肢疼痛性水肿就诊,确诊为嗜酸性筋膜炎(EF)。他也符合高嗜酸性粒细胞综合征(HES)的标准,但尽管进行了仔细检查,仍没有发现提示恶性肿瘤或血液系统肿瘤的迹象。他开始接受类固醇治疗,但随后出现严重的肝功能障碍、噬血细胞性淋巴组织细胞增生症、肝脾肿大和肾脏受累。最终通过骨髓复查和肝活检诊断为外周 T 细胞淋巴瘤,非特指型。在嗜酸性粒细胞增多、EF 和/或 HES 的情况下,重要的是要怀疑存在内在异常,包括潜在的 T 细胞淋巴瘤。