Chouchene Farah, Ben Haj Khalifa Aymen, Masmoudi Fatma, Baaziz Ahlem, Maatouk Fethi, Ghedira Hichem
Pediatric and Preventive Dentistry Department, Faculty of Dental Medicine of Monastir, Laboratory of Biological, Clinical and Dento-Facial Approach, University of Monastir, Monastir, Tunisia.
Department of Dental Anatomy, Faculty of Dental Medicine, University of Monastir, Monastir, Tunisia.
Case Rep Dent. 2022 Apr 22;2022:9585460. doi: 10.1155/2022/9585460. eCollection 2022.
Sanjad-Sakati syndrome (SSS) is a rare autosomal recessive congenital disorder. The present case report is aimed at describing the orofacial manifestations and dental management of a 4-year seven-month-old, Tunisian boy with SSS. The patient has typical dysmorphic facial features and growth retardation. Intraoral examination revealed micrognathic mandible and maxilla, an arched palate, and small dental arches with an open bite. All the maxillary and mandibular teeth were decayed due to the poor oral hygiene, plaque accumulation, and enamel hypoplasia. Oral rehabilitation involved pulpotomies and root canal therapies on decayed teeth. Resin composite restorations were performed on maxillary and mandibular incisors, and stainless-steel crowns were placed on maxillary and mandibular first and second primary molars. Dental treatment of children with SSS should improve their quality of life and their general health. Undeveloped dental arches associated with dental anomalies as well as learning deficit make very difficult of the oral rehabilitation of such patients.
桑贾德 - 萨卡蒂综合征（SSS）是一种罕见的常染色体隐性先天性疾病。本病例报告旨在描述一名4岁7个月大的突尼斯男孩患SSS时的口面部表现及牙科治疗情况。该患者具有典型的面部畸形特征和生长发育迟缓。口腔检查发现下颌骨和上颌骨发育不全、腭弓高拱、牙弓小且开牙合。由于口腔卫生差、菌斑堆积和釉质发育不全，所有上颌和下颌牙齿均有龋坏。口腔修复治疗包括对龋坏牙齿进行牙髓切断术和根管治疗。对上颌和下颌切牙进行了树脂复合材料修复，并在上颌和下颌第一、二乳磨牙上放置了不锈钢冠。对患有SSS的儿童进行牙科治疗应改善他们的生活质量和整体健康状况。与牙齿异常以及学习障碍相关的未发育牙弓使得此类患者的口腔修复非常困难。
