Platis Cari M, Wasersprung David, Kachko Ludmyla, Tsunzer Igor, Katz Jacob
Department of Anesthesia, Schneider Children's Medical Center of Israel, Tel Aviv, Israel.
Paediatr Anaesth. 2006 Nov;16(11):1189-92. doi: 10.1111/j.1460-9592.2006.01981.x.
Sanjad-Sakati syndrome (SSS) is a rare genetic disorder characterized by congenital hypoparathyroidism, hypocalcemia and hyperphosphatemia, seizures, severe intrauterine and postnatal growth failure, dwarfism, mental retardation, dysmorphic features including retromicrognathia and abnormal dentition and increased susceptibility to infection. It is mainly confined to children in the Middle-East countries. We report the anesthesia management of a 12-year-old boy with SSS for dental treatment, and discuss the anesthesia implications of this disorder.
桑贾德 - 萨卡蒂综合征(SSS)是一种罕见的遗传性疾病,其特征为先天性甲状旁腺功能减退、低钙血症和高磷血症、癫痫发作、严重的宫内和出生后生长发育迟缓、侏儒症、智力障碍、包括小颌后缩和牙齿异常在内的畸形特征以及易感染性增加。它主要见于中东国家的儿童。我们报告了一名患有SSS的12岁男孩接受牙科治疗时的麻醉管理,并讨论了该疾病的麻醉相关问题。