Departments of Oral and Maxillofacial Surgery, Oral Medicine and Periodontology, School of Dentistry, The University of Jordan, Amman, Jordan.
Department of Dentistry, The University of Jordan Hospital, Amman, Jordan.
Med Princ Pract. 2018;27(3):293-296. doi: 10.1159/000488352. Epub 2018 Mar 13.
The aim of this report is to describe the orofacial manifestations and dental management of a girl with Sanjad-Sakati syndrome.
The facial features included microcephaly, thin lips, beaked nose, low set ears, and a retrognathic mandible. An oral examination revealed oligodontia/hypodontia, small dental arches, a high arched palate, and a deep overbite and increased overjet. Oral rehabilitation involved full coverage prosthetic crowns on the upper central incisors, stainless steel crowns on the lower molars, and removable partial prostheses to replace missing teeth.
Recognition of orofacial features might help in the diagnosis of Sanjad-Sakati syndrome. Dental management of affected patients might be complicated by intellectual, neurological, and endocrine abnormalities.
本报告旨在描述一名患有 Sanjad-Sakati 综合征女孩的口腔颌面部表现和牙科管理。
面部特征包括小头畸形、薄唇、鹰钩鼻、低位耳和后缩下颌。口腔检查发现牙列稀疏/缺牙、小牙弓、高拱形腭和深覆合及深覆盖。口腔修复包括在上颌中切牙上进行全冠修复、在下颌磨牙上进行不锈钢冠修复以及用可摘局部义齿来替代缺失的牙齿。
识别口腔颌面部特征有助于诊断 Sanjad-Sakati 综合征。受影响患者的牙科管理可能因智力、神经和内分泌异常而变得复杂。