Naik Piyu Parth
Department of Dermatology, Saudi German Hospital and Clinic, Opposite Burj Al Arab, Dubai, United Arab Emirates.
J Transl Autoimmun. 2022 Apr 16;5:100156. doi: 10.1016/j.jtauto.2022.100156. eCollection 2022.
Bruton tyrosine kinase (BTK) is involved in a multifarious inflammatory and autoimmune process. As a result, BTK has emerged as a promising novel remedial target for amalgamated autoimmune diseases. Medicament corporations have recently devoted considerable attention to the evolution of BTK inhibitors. Pemphigus is an uncommon and often fatal autoimmune illness. Blisters and erosions on cutaneous surfaces and mucous membranes are crippling symptoms of pemphigus vulgaris, which are caused by immunoglobulin G autoantibodies binding to keratinocyte proteins, resulting in keratinocyte adhesion defects. Although systemic corticosteroids and adjuvant medications are used to treat pemphigus, some patients are resistant to these. BTK inhibitors inhibit B-cell signaling, which is clinically useful in treating pemphigus. Assorted clinical trials are underway to assess the safety, tolerability, and pharmacokinetics of distinct BTK inhibitors, including PRN473 and remibrutinib. The current review evaluates translational autoimmunity in pemphigus and discusses BTK inhibitors in the treatment of pemphigus.
布鲁顿酪氨酸激酶(BTK)参与多种炎症和自身免疫过程。因此,BTK已成为治疗合并自身免疫性疾病的一个有前景的新型治疗靶点。制药公司最近对BTK抑制剂的研发投入了大量关注。天疱疮是一种罕见且往往致命的自身免疫性疾病。皮肤表面和黏膜上的水疱和糜烂是寻常型天疱疮的致残症状,这是由免疫球蛋白G自身抗体与角质形成细胞蛋白结合导致角质形成细胞黏附缺陷引起的。尽管全身用皮质类固醇和辅助药物用于治疗天疱疮,但一些患者对此耐药。BTK抑制剂抑制B细胞信号传导,这在治疗天疱疮方面具有临床应用价值。正在进行各种临床试验以评估不同BTK抑制剂(包括PRN473和瑞布替尼)的安全性、耐受性和药代动力学。本综述评估了天疱疮中的转化自身免疫,并讨论了BTK抑制剂在天疱疮治疗中的应用。