Department of Pediatrics, Geneva University Hospitals, Willy-Donzé Street 6, 1205 Geneva, Switzerland.
Department of Pediatrics, Geneva University Hospitals, Willy-Donzé Street 6, 1205 Geneva, Switzerland.
Arch Pediatr. 2022 Jul;29(5):398-403. doi: 10.1016/j.arcped.2022.03.006. Epub 2022 May 4.
Postural tachycardia syndrome (PoTS) is a polymorphic clinical syndrome that is underdiagnosed, especially in adolescents. It is a form of dysautonomia, but its exact physiopathology remains elusive. Several pathologies can mimic PoTS; it is characterized by heterogeneous symptoms that accompany a disproportionate tachycardia upon the upright position. It can significantly impact the patients' quality of life. Only a Schellong test is useful for making the diagnosis. Treatment in PoTS is primarily symptomatic with the main goal being to restore the patient's condition as quickly as possible. We report here the diagnosis and management of seven adolescents, aged 11-16, who have been followed up since 2015.
体位性心动过速综合征（PoTS）是一种多态性临床综合征，尤其在青少年中易被漏诊。它是一种自主神经功能障碍的形式，但确切的病理生理学仍不清楚。几种病理学可以模拟 PoTS；其特征是伴随直立位时不成比例的心动过速出现的异质症状。它会显著影响患者的生活质量。只有 Schellong 测试对做出诊断有帮助。PoTS 的治疗主要是对症治疗，主要目标是尽快恢复患者的状况。我们在此报告自 2015 年以来一直随访的 7 名年龄在 11-16 岁的青少年的诊断和治疗情况。
