AlGhadeer Huda
King Khaled Eye Specialist Hospital, Riyadh, Saudi Arabia.
Case Rep Ophthalmol Med. 2022 May 9;2022:6366949. doi: 10.1155/2022/6366949. eCollection 2022.
Anterior megalophthalmos is a rare, bilateral, nonprogressive, hereditary, congenital disorder characterized by the enlargement of all anterior segment structures of the eye, with megalocornea, iris atrophy, and zonular abnormalities. We report a case of an 8-year-old male who presented to the emergency department with a history of visual loss after a blunt ocular trauma to the left eye. The patient presented with markedly enlarged corneas and deepened anterior chambers bilaterally. Best-corrected visual acuity (BCVA) was hand motion in the left eye. An additional examination revealed multiple anterior segment abnormalities, leading to the diagnosis of megalophthalmos and lens dislocation in the anterior chamber. The patient underwent a lensectomy and anterior vitrectomy in the left eye. At six months postoperatively, the BCVA was 20/200 in the left eye. Lens dislocation in patients with megalocornea is rare. Cataract surgery in these patients requires attention to the zonular abnormalities and lens enlargement, resulting in increased rates of intraoperative and postoperative complications. Ophthalmologists should be able to diagnose this rare disorder and manage the associations and complications.
前部巨眼症是一种罕见的、双侧性、非进行性、遗传性先天性疾病，其特征为眼部所有前段结构增大，伴有大角膜、虹膜萎缩和悬韧带异常。我们报告一例8岁男性患者，因左眼钝挫伤后视力丧失前来急诊科就诊。患者双侧角膜明显增大，前房加深。左眼最佳矫正视力（BCVA）为手动。进一步检查发现多个前段异常，诊断为前部巨眼症和晶状体脱位至前房。该患者左眼接受了晶状体切除术和前部玻璃体切除术。术后6个月，左眼BCVA为20/200。大角膜患者发生晶状体脱位较为罕见。这些患者的白内障手术需要注意悬韧带异常和晶状体增大，从而导致术中及术后并发症发生率增加。眼科医生应能够诊断这种罕见疾病并处理相关情况及并发症。
