Department of Ophthalmology, College of Medicine, Imam Abdulrahman Bin Faisal University, Dammam, Saudi Arabia.
Department of Ophthalmology, College of Medicine, King Saud University, P.O. Box 245, Riyadh, 11411, Saudi Arabia.
BMC Ophthalmol. 2022 May 23;22(1):232. doi: 10.1186/s12886-022-02429-4.
Intramuscular haemangiomas are rare, benign vascular tumours that represent < 1% of all haemangiomas. When involving the extraocular muscles, haemangiomas are extremely rare, with only nine cases reported in the literature; to date there are no reported cases of extraocular muscle haemangiomas extending into the brain.
A 6-year-old boy with a two-week history of a painless swelling and erythema on the upper eyelid. On examination, the patient had restricted extraocular motility in all directions of gaze. In addition, the eye appeared proptotic, with chemosis and hyperaemia of the conjunctiva. Visual acuity and intraocular pressure were normal. Orbital computed tomography imaging showed a mass in the left superior rectus, with heterogeneous enhancement following contrast administration. Incisional biopsy revealed an intramuscular haemangioma of the superior rectus muscle with capillary-type vessels. The patient received an intralesional steroid, which improved the condition for a few months; however, the lesion later recurred and included an intracranial extension.
This case represents the first reported case of intracranial extension of intramuscular haemangioma of extraocular muscle.
肌内血管瘤是罕见的良性血管肿瘤，占所有血管瘤的<1%。当涉及眼外肌时，血管瘤极为罕见，文献中仅报道了 9 例；迄今为止，尚无眼外肌血管瘤延伸至大脑的报道。
一名 6 岁男孩，上眼睑有两周的无痛性肿胀和红斑。检查时，患者的眼球各向运动受限。此外，眼睛突出，结膜水肿和充血。视力和眼压正常。眼眶计算机断层扫描显示左眼上直肌有一肿块，增强扫描后呈不均匀强化。切开活检显示上直肌内有毛细血管型血管的肌内血管瘤。患者接受了局部类固醇治疗，病情在几个月内有所改善；然而，病变后来复发并包括颅内延伸。
本例代表了首例报道的眼外肌肌内血管瘤颅内延伸的病例。
