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[成人期诊断出的先天性肺气道畸形]

[Congenital Pulmonary Airway Malformation Diagnosed in Adulthood].

作者信息

Fujita Tomohiro, Kobayashi Kazuma, Eba Shunsuke, Satou Nobuyuki

机构信息

Department of Thoracic Surgery, Aomori Prefectural Central Hospital, Aomori, Japan.

出版信息

Kyobu Geka. 2022 Jun;75(6):432-435.

Abstract

Congenital pulmonary airway malformation diagnosed in adulthood is very rare. A 54-year-old woman was admitted to our hospital with complaints of abnormal chest shadow. Computed tomography( CT) demonstrated multiple cysts, mass lesions, and consolidation in left lower lobe. Bronchofiber scopy could not establish the diagnose. Left lower lobectomy was performed for diagnosis and treatment. Pathologically the lesion was diagnosed as congenital pulmonary airway malformation.

摘要

成人期诊断出的先天性肺气道畸形非常罕见。一名54岁女性因胸部阴影异常而入住我院。计算机断层扫描(CT)显示左肺下叶有多个囊肿、肿块病变和实变。纤维支气管镜检查未能确诊。为明确诊断并进行治疗,实施了左肺下叶切除术。病理检查将该病变诊断为先天性肺气道畸形。

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