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Pan Afr Med J. 2022 Mar 8;41:185. doi: 10.11604/pamj.2022.41.185.30907. eCollection 2022.
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本文引用的文献

1
Prevalence and risk factors for congenital diaphragmatic hernia: A global view.先天性膈疝的患病率和危险因素:全球视角。
J Pediatr Surg. 2020 Nov;55(11):2297-2307. doi: 10.1016/j.jpedsurg.2020.06.022. Epub 2020 Jun 20.
2
Epidemiology and Prognosis of Congenital Diaphragmatic Hernia: A Population-Based Cohort Study in Utah.先天性膈疝的流行病学和预后:犹他州的一项基于人群的队列研究。
Birth Defects Res. 2017 Nov 1;109(18):1451-1459. doi: 10.1002/bdr2.1106. Epub 2017 Sep 19.
3
Epidemiology of congenital diaphragmatic hernia in Europe: a register-based study.欧洲先天性膈疝的流行病学:一项基于登记处的研究。
Arch Dis Child Fetal Neonatal Ed. 2015 Mar;100(2):F137-44. doi: 10.1136/archdischild-2014-306174. Epub 2014 Nov 19.
4
Congenital diaphragmatic hernia.先天性膈疝
J Paediatr Child Health. 2014 Sep;50(9):667-73. doi: 10.1111/jpc.12508. Epub 2014 Feb 17.
5
Late-presenting congenital diaphragmatic hernia in children: the experience of single institution in Korea.韩国单机构诊治的迟发型先天性膈疝患儿:经验总结。
Yonsei Med J. 2013 Sep;54(5):1143-8. doi: 10.3349/ymj.2013.54.5.1143.
6
Outcomes of congenital diaphragmatic hernia: a 12-year experience.先天性膈疝的结局:12 年经验。
Prenat Diagn. 2012 Jun;32(6):523-9. doi: 10.1002/pd.3841. Epub 2012 Apr 13.
7
Late-presenting congenital diaphragmatic hernia: diagnostic pitfalls and outcome.迟发性先天性膈疝:诊断误区与结局。
Hernia. 2012 Aug;16(4):461-6. doi: 10.1007/s10029-012-0906-5. Epub 2012 Mar 7.
8
Congenital diaphragmatic hernia.先天性膈疝。
Orphanet J Rare Dis. 2012 Jan 3;7:1. doi: 10.1186/1750-1172-7-1.
9
Minimally invasive repair of congenital diaphragmatic hernia.先天性膈疝的微创修复。
J Pediatr Surg. 2011 Jun;46(6):1158-64. doi: 10.1016/j.jpedsurg.2011.03.050.
10
Challenges in the management of early versus late presenting congenital diaphragmatic hernia in a poor resource setting.
Afr J Paediatr Surg. 2011 Jan-Apr;8(1):29-33. doi: 10.4103/0189-6725.78665.

[撒哈拉以南非洲地区先天性膈疝的管理:塞内加尔阿尔贝·罗耶国家儿童医院中心的经验]

[Management of congenital diaphragmatic hernia in sub-Saharan Africa: experience in the Albert Royer National Children's Hospital Center, Senegal].

作者信息

Mbaye Papa Alassane, Gueye Doudou, Fall Mbaye, Zeng Florent Tshibwid A, Seye Cheikh, Seck Ndeye Fatou, Cissé Lissoune, Ndoye Ndeye Aby, Sagna Aloïse, Ngom Gabriel

机构信息

Service de Chirurgie Pédiatrique, Hôpital d'Enfants Alber Royer, Université Cheikh Anta Diop, Dakar, Sénégal.

Service de Chirurgie Pédiatrique, Hôpital Aristide Le Dantec, Université Cheikh Anta Diop, Dakar, Sénégal.

出版信息

Pan Afr Med J. 2022 Mar 8;41:185. doi: 10.11604/pamj.2022.41.185.30907. eCollection 2022.

DOI:10.11604/pamj.2022.41.185.30907
PMID:35655674
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9120748/
Abstract

INTRODUCTION

congenital diaphragmatic hernia has been rarely reported in Africa. It can manifests early or late. Prognosis mainly depends on associated malformations. The purpose of this study is to report our experience in the Albert Royer National Children's Hospital, Dakar, Senegal.

METHODS

we conducted a retrospective study of patients treated for congenital diaphragmatic hernia between January 2010 and December 2019.

RESULTS

twelve patients were enrolled, with an average age of 8.9 months. Bochdalek hernias were detected in 10 patients. The most common symptoms were respiratory symptoms (83.3%), followed by digestive symptoms (41.6%). Thoraco-abdominal X-ray was used to make a diagnosis in all patients. Three patients underwent preoperative stabilization. All patients underwent laparotomy. Hernia sac was found in 10 patients, and 50% of patients had a defect measuring between 5 and 10 cm. The postoperative course was simple in 10 patients; a polymalformed patient died.

CONCLUSION

congenital diaphragmatic hernia is a reality in our environment; it most often manifests beyond the neonatal period. Prognosis is generally good in our context.

摘要

引言

先天性膈疝在非洲鲜有报道。其可早发或晚发。预后主要取决于相关畸形。本研究旨在报告我们在塞内加尔达喀尔阿尔贝·罗耶国家儿童医院的经验。

方法

我们对2010年1月至2019年12月期间接受先天性膈疝治疗的患者进行了回顾性研究。

结果

共纳入12例患者,平均年龄8.9个月。10例患者检测出波氏孔疝。最常见症状为呼吸道症状(83.3%),其次为消化道症状(41.6%)。所有患者均通过胸腹部X线进行诊断。3例患者术前行稳定治疗。所有患者均接受剖腹手术。10例患者发现疝囊,50%的患者缺损在5至10厘米之间。10例患者术后病程简单;1例多发畸形患者死亡。

结论

先天性膈疝在我们的环境中是现实存在的;它最常在新生儿期后出现。在我们的情况下,预后总体良好。