Keita Papus, Janko Matthew, Peterman Nicholas J, Toledo Sandor, Pelletier Marc
Surgery, Carle Foundation Hospital, Urbana, USA.
Cardiac Surgery, University Hospitals Cleveland Medical Center, Cleveland, USA.
Cureus. 2022 May 4;14(5):e24734. doi: 10.7759/cureus.24734. eCollection 2022 May.
Leiomyosarcoma of the pulmonary artery is a rare but potentially fatal disease. Due to its rarity, the treatment algorithm is not well-established. While there may be a role for both chemotherapy and radiotherapy, surgical management is the most definitive method. Unfortunately, when the disease process is advanced, surgery may not be curative. However, it may still be a palliative treatment option. In this case report, we present a patient who suffered from respiratory symptoms that were initially attributed to pulmonary embolism (PE). However, upon the diagnosis of pulmonary artery leiomyosarcoma (PAL), surgery intervention was undertaken and resulted in an improved quality of life for the patient.
肺动脉平滑肌肉瘤是一种罕见但可能致命的疾病。由于其罕见性，治疗方案尚未完全确立。虽然化疗和放疗可能都有一定作用，但手术治疗是最具决定性的方法。不幸的是，当疾病进展到晚期时，手术可能无法治愈。然而，它仍然可能是一种姑息性治疗选择。在本病例报告中，我们介绍了一名患者，其最初出现的呼吸道症状被归因于肺栓塞（PE）。然而，在诊断为肺动脉平滑肌肉瘤（PAL）后，进行了手术干预，患者的生活质量得到了改善。
