Nepal Medical College and Teaching Hospital, Attarkhel, Kathmandu, Nepal.
Department of Neurosurgery, Kathmandu Medical College and Teaching Hospital, Sinamangal, Kathmandu, Nepal.
JNMA J Nepal Med Assoc. 2022 Jun 1;60(250):551-554. doi: 10.31729/jnma.7410.
Cerebral hemangiopericytomas are very rare mesenchymal tumours arising from pericytes surrounding the blood vessels in the brain. Most patients present with headaches, focal neurological findings and focal seizures with or without generalisation. Our patient chiefly complained of an uncontrollable movement of her right hand that was initially fleeting but later became continuous. Her symptoms were initially described as tremors. We found an intracranial tumour as a cause of her symptoms, suspected the tumour to be a meningioma and performed surgical extirpation which resulted in symptom resolution. Histopathology and immunohistochemistry of the excised mass revealed that the tumour was hemangiopericytoma. The patient is being closely monitored for recurrences and metastasis. Hemangiopericytomas are very rare and they rarely result in the abnormal movements of epilepsia partialis continua. Differentiation of the abnormal movements of epilepsia partialis continua from tremors is very important as is the differentiation of the tumour from meningioma.
case reports; epilepsia partialis continua; hemangiopericytoma; solitary fibrous tumors.
脑血管外皮细胞瘤是一种非常罕见的间叶性肿瘤，起源于脑内血管周围的周细胞。大多数患者表现为头痛、局灶性神经功能障碍和局灶性癫痫发作，伴有或不伴有全身性发作。我们的患者主要抱怨右手无法控制的运动，最初是短暂的，但后来变得持续。她的症状最初被描述为震颤。我们发现颅内肿瘤是她症状的原因，怀疑肿瘤是脑膜瘤，并进行了手术切除，症状得到缓解。切除肿块的组织病理学和免疫组织化学检查显示肿瘤为血管外皮细胞瘤。患者正在密切监测复发和转移情况。血管外皮细胞瘤非常罕见，很少导致部分连续性癫痫的异常运动。区分部分连续性癫痫的异常运动与震颤非常重要，区分肿瘤与脑膜瘤也非常重要。
病例报告；部分连续性癫痫；血管外皮细胞瘤；孤立性纤维瘤。
