• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

慢性炎症性脱髓鞘性多发性神经根神经病:五个新进展

Chronic Inflammatory Demyelinating Polyradiculoneuropathy: Five New Things.

作者信息

Karam Chafic

机构信息

Department of Neurology, University of Pennsylvania, Philadelphia.

出版信息

Neurol Clin Pract. 2022 Jun;12(3):258-262. doi: 10.1212/CPJ.0000000000001150.

DOI:10.1212/CPJ.0000000000001150
PMID:35747539
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9208411/
Abstract

PURPOSE OF REVIEW

The purpose of this review is to give an update on chronic inflammatory demyelinating polyradiculoneuropathy (CIDP).

RECENT FINDINGS

There are several recent developments in CIDP, the major one being the 2021 second revision of the European Academy of Neurology/Peripheral Nerve Society guideline on diagnosis and treatment of chronic inflammatory demyelinating polyradiculoneuropathy. Other updates address therapy in CIDP, antibodies, serum neurofilament light chain, chronic immune sensory polyradiculopathy (CISP) and CIDP mimics.

SUMMARY

CIDP criteria continue to be refined and some disorders are now excluded from the classification. Treatment options are expending and promising biomarkers are being studied.

摘要

综述目的

本综述旨在提供慢性炎性脱髓鞘性多发性神经根神经病(CIDP)的最新进展。

最新发现

CIDP近期有多项进展,主要的一项是2021年欧洲神经病学学会/周围神经学会关于慢性炎性脱髓鞘性多发性神经根神经病诊断和治疗指南的第二次修订。其他更新内容涉及CIDP的治疗、抗体、血清神经丝轻链、慢性免疫感觉性多发性神经根病(CISP)以及CIDP的模仿疾病。

总结

CIDP的诊断标准在不断完善,一些疾病现在已被排除在分类之外。治疗选择在不断扩展,并且正在研究有前景的生物标志物。

相似文献

1
Chronic Inflammatory Demyelinating Polyradiculoneuropathy: Five New Things.慢性炎症性脱髓鞘性多发性神经根神经病:五个新进展
Neurol Clin Pract. 2022 Jun;12(3):258-262. doi: 10.1212/CPJ.0000000000001150.
2
European Academy of Neurology/Peripheral Nerve Society guideline on diagnosis and treatment of chronic inflammatory demyelinating polyradiculoneuropathy: Report of a joint Task Force-Second revision.欧洲神经病学学会/周围神经学会关于慢性炎症性脱髓鞘性多发性神经病的诊断和治疗指南:联合工作组的报告——第二次修订版。
Eur J Neurol. 2021 Nov;28(11):3556-3583. doi: 10.1111/ene.14959. Epub 2021 Jul 30.
3
European Academy of Neurology/Peripheral Nerve Society guideline on diagnosis and treatment of chronic inflammatory demyelinating polyradiculoneuropathy: Report of a joint Task Force-Second revision.欧洲神经病学会/周围神经学会慢性炎症性脱髓鞘性多发性神经病诊断和治疗指南:联合工作组报告——第二次修订版。
J Peripher Nerv Syst. 2021 Sep;26(3):242-268. doi: 10.1111/jns.12455. Epub 2021 Jul 30.
4
Tips in navigating the diagnostic complexities of chronic inflammatory demyelinating polyradiculoneuropathy.慢性炎症性脱髓鞘性多发性神经根神经病诊断复杂性的应对技巧。
J Neurol Sci. 2022 Dec 15;443:120478. doi: 10.1016/j.jns.2022.120478. Epub 2022 Oct 27.
5
Chronic inflammatory demyelinating polyradiculoneuropathy and variants: where we are and where we should go.慢性炎症性脱髓鞘性多发性神经根神经病及其变异型:我们所处的位置与前进方向
J Peripher Nerv Syst. 2014 Mar;19(1):2-13. doi: 10.1111/jns5.12053.
6
Application of the 2021 EAN/PNS criteria for chronic inflammatory demyelinating polyneuropathy.2021 年 EAN/PNS 慢性炎症性脱髓鞘性多发性神经病标准的应用。
J Neurol Neurosurg Psychiatry. 2022 Dec;93(12):1247-1252. doi: 10.1136/jnnp-2022-329633. Epub 2022 Sep 8.
7
Chronic immune sensory polyradiculopathy (CISP): First juvenile case description.慢性免疫性感觉性多神经根病(CISP):首例青少年病例描述。
Neurol Sci. 2021 Jan;42(1):333-336. doi: 10.1007/s10072-020-04588-y. Epub 2020 Jul 10.
8
Chronic inflammatory demyelinating polyradiculoneuropathy: can a diagnosis be made in patients not fulfilling electrodiagnostic criteria?慢性炎症性脱髓鞘性多发神经病:不符合电诊断标准的患者能否做出诊断?
Eur J Neurol. 2021 Feb;28(2):620-629. doi: 10.1111/ene.14545. Epub 2020 Oct 15.
9
Comparison of the diagnostic accuracy of the 2021 EAN/PNS and 2010 EFNS/PNS diagnostic criteria for chronic inflammatory demyelinating polyradiculoneuropathy.2021EAN/PNS 与 2010EFNS/PNS 慢性炎症性脱髓鞘性多发性神经病诊断标准的诊断准确性比较。
J Neurol Neurosurg Psychiatry. 2022 Dec;93(12):1239-1246. doi: 10.1136/jnnp-2022-329357. Epub 2022 Sep 8.
10
Challenges in the Early Diagnosis and Treatment of Chronic Inflammatory Demyelinating Polyradiculoneuropathy in Adults: Current Perspectives.成人慢性炎性脱髓鞘性多发性神经根神经病早期诊断与治疗面临的挑战:当前观点
Ther Clin Risk Manag. 2024 Feb 14;20:111-126. doi: 10.2147/TCRM.S360249. eCollection 2024.

引用本文的文献

1
Neurofilaments as biomarkers in neurological disorders - towards clinical application.神经丝作为神经紊乱的生物标志物——迈向临床应用。
Nat Rev Neurol. 2024 May;20(5):269-287. doi: 10.1038/s41582-024-00955-x. Epub 2024 Apr 12.
2
The 2022 Lady Estelle Wolfson lectureship on neurofilaments.2022 年埃斯特尔·沃尔夫森夫人神经丝讲座。
J Neurochem. 2022 Nov;163(3):179-219. doi: 10.1111/jnc.15682. Epub 2022 Sep 19.

本文引用的文献

1
European Academy of Neurology/Peripheral Nerve Society guideline on diagnosis and treatment of chronic inflammatory demyelinating polyradiculoneuropathy: Report of a joint Task Force-Second revision.欧洲神经病学学会/周围神经学会关于慢性炎症性脱髓鞘性多发性神经病的诊断和治疗指南:联合工作组的报告——第二次修订版。
Eur J Neurol. 2021 Nov;28(11):3556-3583. doi: 10.1111/ene.14959. Epub 2021 Jul 30.
2
Subcutaneous immunoglobulin treatment for chronic inflammatory demyelinating polyneuropathy.皮下免疫球蛋白治疗慢性炎症性脱髓鞘性多发性神经病。
Muscle Nerve. 2021 Sep;64(3):243-254. doi: 10.1002/mus.27356. Epub 2021 Jul 14.
3
Clinical outcome of CIDP one year after start of treatment: a prospective cohort study.治疗开始后 1 年 CIDP 的临床转归:一项前瞻性队列研究。
J Neurol. 2022 Feb;269(2):945-955. doi: 10.1007/s00415-021-10677-5. Epub 2021 Jun 26.
4
Misdiagnosis and diagnostic pitfalls of chronic inflammatory demyelinating polyradiculoneuropathy.慢性炎症性脱髓鞘性多发性神经根神经病的误诊及诊断陷阱
Eur J Neurol. 2021 Jun;28(6):2065-2073. doi: 10.1111/ene.14796. Epub 2021 Apr 9.
5
Expanding the Spectrum of Chronic Immune Sensory Polyradiculopathy: CISP-Plus.慢性免疫感觉性多神经根神经病谱的扩展:CISP-Plus。
Neurology. 2021 Apr 20;96(16):e2078-e2089. doi: 10.1212/WNL.0000000000011792. Epub 2021 Mar 2.
6
CIDP mimics: a case series.慢性炎症性脱髓鞘性多发性神经病的模仿疾病:病例系列
BMC Neurol. 2021 Feb 28;21(1):94. doi: 10.1186/s12883-021-02118-7.
7
Refractory CIDP: Clinical characteristics, antibodies and response to alternative treatment.难治性 CIDP:临床特征、抗体及对替代治疗的反应。
J Neurol Sci. 2020 Nov 15;418:117098. doi: 10.1016/j.jns.2020.117098. Epub 2020 Aug 15.
8
Antibodies against the node of Ranvier: a real-life evaluation of incidence, clinical features and response to treatment based on a prospective analysis of 1500 sera.抗郎飞结抗体:基于 1500 份血清的前瞻性分析,对发病率、临床特征和治疗反应的真实评估。
J Neurol. 2020 Dec;267(12):3664-3672. doi: 10.1007/s00415-020-10041-z. Epub 2020 Jul 16.
9
Rituximab in refractory chronic inflammatory demyelinating polyneuropathy.利妥昔单抗治疗难治性慢性炎症性脱髓鞘性多发性神经病。
Muscle Nerve. 2020 May;61(5):575-579. doi: 10.1002/mus.26804. Epub 2020 Jan 21.
10
Long-term safety and efficacy of subcutaneous immunoglobulin IgPro20 in CIDP: PATH extension study.IgPro20 皮下免疫球蛋白治疗 CIDP 的长期安全性和有效性:PATH 扩展研究。
Neurol Neuroimmunol Neuroinflamm. 2019 Jul 3;6(5):e590. doi: 10.1212/NXI.0000000000000590. eCollection 2019 Sep.