Dr Din-E-Mujahid Mohammad Faruque Osmany, Medical Officer, Department of Cardiology, University Cardiac Center (UCC), Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh; E-mail:
Mymensingh Med J. 2022 Jul;31(3):876-881.
Arrhythmogenic right ventricular dysplasia (ARVD) is a progressive degeneration and replacement of the right ventricular (RV) myocardial tissue by fat and fibrosis and produce clinical condition. Desmosome gene mutations are only the causative state for ARVD hereditary disorder. The arrhythmogenic right ventricular cardiomyopathy incidence is about 1/1000-5000. Mostly young people and athletes are bearing the clinical presentations include presyncope, syncope, ventricular tachycardias or ventricular fibrillation leading to cardiac arrest. We report about the first case of Cardiac magnetic resonance (CMR) imaging to diagnose a case Arrhythmogenic right ventricular dysplasia (ARVD) of a 34-year-old male from Savar, Dhaka, Bangladesh who was referred to cardiac emergency for the evaluation recurrent dizzy spells.
致心律失常性右室心肌病(ARVD)是一种右心室(RV)心肌组织进行性变性和被脂肪和纤维组织取代并产生临床症状的疾病。桥粒蛋白基因突变仅是 ARVD 遗传性疾病的致病状态。致心律失常性右室心肌病的发病率约为 1/1000-5000。大多数年轻人和运动员出现临床表现,包括晕厥前状态、晕厥、室性心动过速或室颤导致心脏骤停。我们报告了首例经心脏磁共振(CMR)成像诊断的病例,该病例为一名 34 岁男性,来自孟加拉国达卡的萨瓦尔,因反复头晕就诊于心脏急症以评估。