Dukmak Osama N, Abualia Sulaiman M S, Meqbil Yara J I, Emar Mohammad, Basal Sharif Issa, Itaidek Saeed
Al-Quds University - Faculty of Medicine, Jerusalem, State of Palestine.
Al-Quds University - Faculty of Medicine, Jerusalem, State of Palestine.
Int J Surg Case Rep. 2022 Jul;96:107371. doi: 10.1016/j.ijscr.2022.107371. Epub 2022 Jun 29.
The rare form and mildest variant of Langerhans cell histiocytosis is eosinophilic granuloma (EG). In the clinical presentation, EG can be monostotic, polyostotic, or can encompass many organs. The parietal bone is the most common location of the skull bones that are affected by EG. So far, there have been no reported cases of EG with skull odor as an unexplained presentation.
An 8-year-old girl presented with a 4 months history of a right parietal bone swelling of the skull with an offensive odor. There was no discharge and no history of vomiting or trauma. An MRI scan of the brain showed swelling with a bone lesion of the right parietal bone. Infection was the source of the swelling and the bad odor. Treatment was done by surgical excision of the lesion.
EG has a variety of presentations and should be suspected when tenderness and local swelling are present. Radiography was found to be helpful in the diagnosis and surgical treatment was done to manage the case.
朗格汉斯细胞组织细胞增多症的罕见形式及最轻微变体是嗜酸性肉芽肿（EG）。在临床表现中，EG可为单骨型、多骨型，或可累及多个器官。顶骨是受EG影响的颅骨中最常见的部位。迄今为止，尚无EG以颅骨异味作为不明表现的病例报道。
一名8岁女孩，有4个月右顶骨颅骨肿胀伴恶臭的病史。无分泌物，无呕吐或外伤史。脑部MRI扫描显示右顶骨有骨病变伴肿胀。感染是肿胀和恶臭的根源。通过手术切除病变进行治疗。
EG有多种表现形式，当出现压痛和局部肿胀时应怀疑该病。X线摄影对诊断有帮助，通过手术治疗处理该病例。
