一名28岁女性外阴孤立性朗格汉斯细胞组织细胞增多症：病例报告及文献简要综述
Isolated Langerhans Cell Histiocytosis of the Vulva in a 28-Year-Old Lady: A Report of a Case and Brief Review of the Literature.
作者信息
Sadati Maryam Sadat, Todarbary Nafiseh, Sari Aslani Fatemeh, Hadibarhaghtalab Maryam
机构信息
Molecular Dermatology Research Center, Shiraz University of Medical Sciences, Shiraz, Iran.
Dermatology Department, Shiraz University of Medical Sciences, Shiraz, Iran.
出版信息
Case Rep Dermatol Med. 2022 Jun 28;2022:8483008. doi: 10.1155/2022/8483008. eCollection 2022.
Langerhans cell histiocytosis (LCH) is a rare, proliferative disorder of Langerhans' cells. The presentation can vary from single organ involvement to multisystem and disseminated in severe cases, affecting children more than adults. Isolated vulvar involvement of LCH in a 28-year-old woman has rarely been described and also there are limited data for diagnosis and treatment. Herein, we report the case of a 28-year-old woman with isolated vulvar LCH, misdiagnosed with herpes simplex infection, successfully treated with thalidomide.
朗格汉斯细胞组织细胞增多症（LCH）是一种罕见的朗格汉斯细胞增殖性疾病。其临床表现多样，可从单器官受累到多系统受累，严重时可播散，儿童比成人更易患病。一名28岁女性孤立性外阴受累的LCH病例鲜有报道，且诊断和治疗的数据也有限。在此，我们报告一例28岁孤立性外阴LCH女性病例，该病例最初被误诊为单纯疱疹感染，最终使用沙利度胺成功治愈。
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