Tirado-Ornelas Héctor Alonso, Olivares-Peña Jorge Luis, Olivares-Camacho Jorge Luis, Santos-Franco Jorge Arturo, Ochoa-González Maurilio Vicente
Department of Neurosurgery, Specialties Hospital, La Raza National Medical Center, Mexican Social Security Institute, Mexico City, Mexico.
Department of Spine Surgery, Angeles del Pedregal Hospital, Mexico City, Mexico.
Surg Neurol Int. 2022 Jul 8;13:294. doi: 10.25259/SNI_525_2022. eCollection 2022.
Hemangioblastomas are benign tumors that develop in the central nervous system. They represent 1.5-2.5% of all intracranial tumors, and about 2-15% of all spinal cord tumors. They are highly associated with von Hippel-Lindau disease.
A 36-year-old female presented with a 4-year history of progressive right upper extremity distal weakness and cervical pain. The magnetic resonance imaging demonstrated a homogeneously, contrast enhancing intradural/intramedullary tumor at C6-C7 with perilesional edema and a syrinx accompanied by a cerebellar cyst with a mural nodule. Surgery included excision of the spinal lesion and decompression and excision of the cerebellar cyst and mural nodule (i.e., median suboccipital craniectomy and cervical C5-C7 laminectomy).
Surgery is the gold standard treatment for symptomatic hemangioblastomas, and surgical approaches should minimize risk.
血管母细胞瘤是发生于中枢神经系统的良性肿瘤。它们占所有颅内肿瘤的1.5%-2.5%，占所有脊髓肿瘤的约2%-15%。它们与冯·希佩尔-林道病高度相关。
一名36岁女性，有4年进行性右上肢远端无力和颈部疼痛病史。磁共振成像显示C6-C7水平有一个均匀强化的硬脊膜内/髓内肿瘤，伴有瘤周水肿和一个空洞，同时伴有一个小脑囊肿及壁结节。手术包括切除脊髓病变、减压以及切除小脑囊肿和壁结节（即枕下正中颅骨切除术和颈椎C5-C7椎板切除术）。
手术是有症状血管母细胞瘤的金标准治疗方法，手术入路应将风险降至最低。
