Department of Anesthesiology and Perioperative Medicine, School of Medicine, University of Alabama at Birmingham, Birmingham, AL, 35294, USA.
Mol Brain. 2022 Jul 20;15(1):64. doi: 10.1186/s13041-022-00949-0.
Previous immunohistochemical studies have shown the expression of KCNQ2 channels at nodes of Ranvier (NRs) of myelinated nerves. However, functions of these channels at NRs remain elusive. In the present study, we addressed this issue by directly applying whole-cell patch-clamp recordings at NRs of rat lumbar spinal ventral nerves in ex vivo preparations. We show that depolarizing voltages evoke large non-inactivating outward currents at NRs, which are partially inhibited by KCNQ channel blocker linopirdine and potentiated by KCNQ channel activator retigabine. Furthermore, linopirdine significantly alters intrinsic electrophysiological properties of NRs to depolarize resting membrane potential, increase input resistance, prolong AP width, reduce AP threshold, and decrease AP amplitude. On the other hand, retigabine significantly decreases input resistance and increases AP rheobase at NRs. Moreover, linopirdine increases excitability at NRs by converting single AP firing into multiple AP firing at many NRs. Saltatory conduction velocity is significantly reduced by retigabine, and AP success rate at high stimulation frequency is significantly increased by linopirdine. Collectively, KCNQ2 channels play a significant role in regulating intrinsic electrophysiological properties and saltatory conduction at NRs of motor nerve fibers of rats. These findings may provide insights into how the loss-of-function mutation in KCNQ2 channels can lead to neuromuscular disorders in human patients.
先前的免疫组织化学研究表明,KCNQ2 通道在有髓神经的郎飞结(NRs)处表达。然而,这些通道在 NRs 处的功能仍不清楚。在本研究中,我们通过在离体制备的大鼠腰脊腹神经 NRs 上直接进行全细胞膜片钳记录来解决这个问题。我们表明,去极化电压在 NRs 处引发大的非失活外向电流,该电流部分被 KCNQ 通道阻断剂利诺吡啶抑制,被 KCNQ 通道激活剂瑞替加滨增强。此外,利诺吡啶显著改变 NRs 的固有电生理特性,使其静息膜电位去极化,增加输入电阻,延长 AP 宽度,降低 AP 阈值,并降低 AP 幅度。另一方面,瑞替加滨显著降低 NRs 的输入电阻,并增加 AP 强度。此外,利诺吡啶通过将单个 AP 放电转换为许多 NRs 的多个 AP 放电来增加 NRs 的兴奋性。瑞替加滨显著降低了跳跃传导速度,而利诺吡啶显著增加了高频刺激时的 AP 成功率。总之,KCNQ2 通道在调节大鼠运动神经纤维 NRs 的固有电生理特性和跳跃传导中起重要作用。这些发现可能为 KCNQ2 通道功能丧失突变如何导致人类患者的神经肌肉疾病提供了线索。