先天性大疱性表皮松解症的围手术期管理。
Perioperative Management of Congenital Epidermolysis Bullosa.
机构信息
Department of Respiratory Surgery, Tokyo Rosai Hospital, Tokyo, Japan.
Department of Respiratory Surgery, Tokyo Rosai Hospital, Tokyo, Japan.
出版信息
Ann Thorac Surg. 2023 Jul;116(1):e1-e4. doi: 10.1016/j.athoracsur.2022.06.045. Epub 2022 Jul 19.
Congenital epidermolysis bullosa is a rare disease that causes blister formation in areas susceptible to mechanical stimulation. We present the case of a patient with congenital epidermolysis bullosa simplex who underwent thoracoscopic surgery for pneumothorax. The postoperative course was uneventful, and the patient was discharged on postoperative day 5. Crusts developed around the blistered skin, which normalized within 2 months postoperatively. General anesthesia and skin management are critical in thoracoscopic surgery for patients with congenital epidermolysis bullosa simplex.
先天性大疱性表皮松解症是一种罕见的疾病，会导致易受机械刺激的部位形成水疱。我们报告了 1 例先天性单纯型大疱性表皮松解症患者因气胸行胸腔镜手术的病例。术后过程顺利，患者于术后第 5 天出院。水疱周围出现结痂，术后 2 个月内恢复正常。对于先天性单纯型大疱性表皮松解症患者，全身麻醉和皮肤管理在胸腔镜手术中至关重要。
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