Wada Naoki, Kuwahara Yuta, Komori Yuya, Furuya Tsubasa, Takahashi Yukihiro
Department of Pediatric Cardiovascular Surgery, Sakakibara Heart Institute, Fuchu, Japan.
Kyobu Geka. 2022 Aug;75(8):607-611.
Congenitally corrected transposition of the great arteries( ccTGA) is a rare complex cardiac anomaly, where the heart twist and the ventricles are reversed during fetal development. Through a double switch operation (DSO), the morphologic left ventricle (LV) can be corrected back to pumping blood for systemic circulation. For successful DSO, the morphologic LV may need training with a pulmonary artery banding (PAB) before surgery. There have been reports of early LV failure in patients who underwent PAB training and a DSO, due to rapid pressure loading on the myocardium. We reported a case of DSO in a 16 years old male after prolonged LV training with a loose PAB. He was scheduled for a DSO, due to severe tricuspid regurgitation( TR). At eight years old, he underwent a loose PAB training with left ventricular pressure to right ventricular pressure ratio (LVp/RVp) of 0.5. After eight years, the LVp/RVp ratio increased to 0.77;he successfully underwent a DSO with good LV function.
先天性矫正型大动脉转位(ccTGA)是一种罕见的复杂心脏畸形,在胎儿发育过程中心脏发生扭转且心室反转。通过双调转手术(DSO),形态学左心室(LV)可恢复为为体循环泵血。为使DSO成功,形态学左心室在手术前可能需要通过肺动脉环扎术(PAB)进行训练。有报道称,接受PAB训练和DSO的患者会出现早期左心室衰竭,原因是心肌承受快速的压力负荷。我们报告了一例16岁男性患者,在使用宽松的PAB进行长时间左心室训练后接受DSO的病例。由于严重的三尖瓣反流(TR),他计划接受DSO。8岁时,他接受了宽松的PAB训练,左心室压力与右心室压力之比(LVp/RVp)为0.5。8年后,LVp/RVp比值增至0.77;他成功接受了DSO,左心室功能良好。