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一种罕见医源性双房Gerbode缺损的诊断与处理

Diagnosis and Management of a Unique Iatrogenic Biatrial Gerbode Defect.

作者信息

Shuaib Karim, Scorsese Giacomo, Seiter Christopher, Zabirowicz Eric, Poppers Jeremy

机构信息

Department of Anesthesiology, Stony Brook University Health Science Center, Stony Brook, NY 11794-8480, USA.

出版信息

Case Rep Anesthesiol. 2022 Jul 18;2022:6998632. doi: 10.1155/2022/6998632. eCollection 2022.

DOI:10.1155/2022/6998632
PMID:35898431
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9313924/
Abstract

The Gerbode defect was first described in the late 1950s as a congenital peri-membranous ventricular septal defect (VSD), resulting in a left to right ventriculoatrial shunt. We present a case of a patient with restenosis of a prior bioprosthetic aortic valve (AV) who underwent reoperative AV replacement (AVR), which was complicated by a unique iatrogenic Gerbode defect with concurrent LV-LA communication. Our case highlights the unique complications resulting from ventriculoatrial shunts, with consideration paid to the management of ventriculoatrial defects described.

摘要

1950年代末首次描述的Gerbode缺损是一种先天性膜周部室间隔缺损(VSD),导致左向右心室心房分流。我们报告一例曾接受生物瓣主动脉瓣(AV)置换术的患者发生再狭窄,该患者接受了再次AV置换术(AVR),术中并发了独特的医源性Gerbode缺损及左心室-左心房交通。我们的病例突出了心室心房分流导致的独特并发症,并对所述心室心房缺损的处理进行了探讨。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/173963b34b70/CRIA2022-6998632.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/32b39f7653b0/CRIA2022-6998632.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/d44dced57eba/CRIA2022-6998632.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/173963b34b70/CRIA2022-6998632.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/32b39f7653b0/CRIA2022-6998632.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/d44dced57eba/CRIA2022-6998632.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/2640/9313924/173963b34b70/CRIA2022-6998632.003.jpg

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Unusual left ventricle to left atrial fistula.左心室至左心房异常瘘管。
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