Kalauz Mirjana, Cukovic Cavka Silvija, Domislovic Viktor, Pourmodjib Kiarash, Kalauz Matija, Dotlic Snjezana, Grubelic Ravic Katja, Krznaric Zeljko
Department of Internal Medicine Division of Gastroenterology, Zagreb University Hospital Center School of Medicine University of Zagreb Zagreb Croatia.
School of Medicine University of Zagreb Zagreb Croatia.
DEN Open. 2022 Jun 20;3(1):e140. doi: 10.1002/deo2.140. eCollection 2023 Apr.
A 48-year-old female patient presented with longstanding unrecognized celiac disease (CD), a family history of CD, and a short duration of alarming symptoms. The diagnostic evaluation revealed the concomitant presence of small and large bowel ulcers raised a dilemma about differential diagnosis in her case. Pathologic examination of tissue specimens from the jejunal ulcer led to the diagnosis of enteropathy-associated T-cell lymphoma. In recent years, the availability of modern cross-sectional imaging and endoscopy modalities has dramatically improved the detection and characterization of small bowel lesions. Characterization of small bowel ulcers by endoscopy and radiology imaging in a patient with suspected complicated CD (CCD) needs to be made in conjunction with all clinical factors, as there is a wide overlap of the possible etiologic factors. Enteropathy-associated T-cell lymphoma is a highly aggressive T-cell lymphoma with a poor prognosis, since early diagnosis and appropriate treatment may be delayed due to nonspecific clinical and endoscopic presentation. Therefore, it is crucial to timely recognize patients with suspected CCD and properly navigate diagnostic imaging tools, acquire adequate biopsy, and perform immunophenotyping to set early diagnosis in patients with diffuse intestinal ulcers and CD.
一名48岁女性患者患有长期未被识别的乳糜泻(CD),有CD家族史,且出现警示症状的时间较短。诊断评估显示,同时存在小肠和大肠溃疡,这给她的鉴别诊断带来了难题。空肠溃疡组织标本的病理检查确诊为肠病相关T细胞淋巴瘤。近年来,现代横断面成像和内镜检查手段的应用显著提高了小肠病变的检测和特征描述能力。对于疑似复杂性CD(CCD)患者,通过内镜检查和放射影像学对小肠溃疡进行特征描述时,需要结合所有临床因素,因为可能的病因因素存在广泛重叠。肠病相关T细胞淋巴瘤是一种侵袭性很强、预后较差的T细胞淋巴瘤,由于其临床和内镜表现不具特异性,早期诊断和适当治疗可能会延迟。因此,及时识别疑似CCD患者并正确运用诊断成像工具、获取足够的活检样本并进行免疫表型分析,以对弥漫性肠道溃疡和CD患者进行早期诊断至关重要。