Abreu da Silva Alberto, Ferreira Andreia, Cusati Pierpaolo, Martins José Augusto
Serviço de Cirurgia Geral. Unidade Local de Saúde do Litoral Alentejano. Santiago do Cacém. Portugal.
Serviço de Anatomia Patológica. Unidade Local de Saúde do Litoral Alentejano. Santiago do Cacém. Portugal.
Acta Med Port. 2023 Apr 3;36(4):278-282. doi: 10.20344/amp.17544. Epub 2022 Aug 1.
Mesenteric schwannomas are rare benign tumors that arise in the mesentery. Ileal diverticula and intestinal malrotation in adults are rare findings, since they are usually asymptomatic. We present the case of an 86-year-old man, without any known previously known medical conditions, who was admitted in the emergency department with recurrent abdominal distension and intense pain. The radiological study suggested an intestinal malrotation. An exploratory laparotomy confirmed the intestinal malrotation with intermesenteric bands, as well as a mesenteric mass adjacent to an ileal diverticulum. Following a segmental enterectomy, the histology of the mass reported a mesenteric schwannoma. To the best of our knowledge, this is the first report of such association. We therefore present this report to showcase the diagnostic and therapeutical challenges in managing these conditions.
肠系膜神经鞘瘤是一种罕见的起源于肠系膜的良性肿瘤。成人回肠憩室和肠旋转不良较为罕见，因为它们通常没有症状。我们报告一例86岁男性病例，既往无任何已知病史，因反复腹胀和剧烈腹痛入住急诊科。影像学检查提示肠旋转不良。剖腹探查证实存在肠旋转不良伴肠系膜间束带，以及一个与回肠憩室相邻的肠系膜肿物。行节段性肠切除术后，肿物组织学检查报告为肠系膜神经鞘瘤。据我们所知，这是此类关联的首例报告。因此，我们呈现此报告以展示处理这些情况时的诊断和治疗挑战。
