Laverdeur Clarice, Azongmo Tadjouteu Murielle, Berenger Ngah Claude, Gorur Yilmaz, Cardos Benoit, Lorenzo Villalba Noel, Ali Deeba
Service des Urgences, CHU Sart-Tilman, Liège, Belgium.
Service des Urgences, CHR Citadelle de Liège, Liège, Belgium.
Eur J Case Rep Intern Med. 2022 Jul 27;9(7):003436. doi: 10.12890/2022_003436. eCollection 2022.
Vertebro-basilar dolichoectasia (VBD) is a rare pathology of unknown aetiology. Its clinical presentation is wide and prognosis is generally poor with a high mortality rate. Cerebral magnetic resonance imaging is the gold standard for diagnosis. We report an unusual case of intracranial dolichoectasia. VBD was revealed during investigation of a patient with altered mental status. CT brain imaging demonstrated severe obstructive hydrocephalus secondary to compression of the third ventricle. Management is always challenging and depends on the location and the mode of presentation. Our patient died despite surgical management with placement of an external ventricular shunt.
Vertebro-basilar dolichoectasia is a little known cause of altered mental status in elderly patients.An atypical presentation of vertebro-basilar dolichoectasia can mimic extensive cerebrovascular haemorrhage.The prognosis is poor despite prompt diagnosis and the surgical treatment of choice.
椎基底动脉延长扩张症(VBD)是一种病因不明的罕见病症。其临床表现多样,预后通常较差,死亡率高。脑磁共振成像是诊断的金标准。我们报告一例颅内延长扩张症的罕见病例。在对一名精神状态改变的患者进行检查时发现了VBD。脑部CT成像显示严重梗阻性脑积水继发于第三脑室受压。治疗一直具有挑战性,取决于病变部位和表现方式。尽管进行了手术治疗并放置了外部脑室分流管,我们的患者仍死亡。
椎基底动脉延长扩张症是老年患者精神状态改变的一个鲜为人知的原因。椎基底动脉延长扩张症的非典型表现可类似广泛的脑血管出血。尽管及时诊断并选择了手术治疗,但其预后仍较差。