Nilesh Kumar, Raje Vinayak, Karambelkar Vijay Hari
Department of Oral and Maxillofacial Surgery, SDS, Krishna Institute of Medical Sciences Deemed to be University, Karad, Maharashtra, India.
Department of Neurosurgery, Krishna Institute of Medical Sciences Deemed to be University, Karad, Maharashtra, India.
Natl J Maxillofac Surg. 2022 May-Aug;13(2):302-306. doi: 10.4103/njms.njms_360_21. Epub 2022 Jun 15.
Schwannomas are rare benign tumors arising from Schwann cells of the nerve sheath. Although the head-and-neck region accounts for a large percentage of extracranial schwannomas, those located within the orbit are infrequent. This paper presents an extremely rare case of orbital schwannoma arising from the terminal branch of abducens nerve in a 37-year-old female. The lesion presented as a large intraconal mass causing proptosis and weakness to abduct the left eye. Imaging showed a well-defined, solid-cystic lesion, measuring 2.7 cm and displacing the lateral rectus muscle laterally and the optic nerve medially. A multidisciplinary approach was used for the surgical management of the tumor. Access was attained through lateral rim osteotomy. Histopathological evaluation was diagnostic for schwannoma. A search of English literature revealed only five previously published cases of abducens nerve schwannomas. A review of these cases has also been discussed along with the present report.
施万细胞瘤是起源于神经鞘雪旺细胞的罕见良性肿瘤。虽然头颈部区域占颅外施万细胞瘤的很大比例，但位于眼眶内的却很少见。本文报告了一例极为罕见的眼眶施万细胞瘤病例，发生于一名37岁女性的展神经终末支。病变表现为眶内巨大肿块，导致左眼突出及外展无力。影像学显示为边界清晰的实性囊性病变，大小为2.7 cm，使外直肌向外移位，视神经向内移位。采用多学科方法对肿瘤进行手术治疗。通过外侧眶缘截骨术进入。组织病理学评估确诊为施万细胞瘤。检索英文文献仅发现5例先前发表的展神经施万细胞瘤病例。本文报告还对这些病例进行了回顾讨论。
