Department of Molecular Medicine and Haematology, Faculty of Health Sciences, University of the Witwatersrand (Wits) and National Health Laboratory Service (NHLS), Johannesburg, South Africa.
Division of Immunology, Department of Pathology, Faculty of Health Sciences, University of the Cape Town (UCT) and National Health Laboratory Service (NHLS), Cape Town, South Africa.
J Clin Apher. 2022 Oct;37(5):460-467. doi: 10.1002/jca.22003. Epub 2022 Aug 20.
Patients with Human Immunodeficiency Virus (HIV) infection are at risk of thrombotic microangiopathies (TMAs) notably thrombotic thrombocytopenic purpura (TTP) and disseminated intravascular coagulation (DIC). Overlap between laboratory results exists resulting in diagnostic ambiguity.
Routine laboratory results of 71 patients with HIV-associated TTP (HIV-TTP) and 81 with DIC with concomitant HIV infection (HIV-DIC) admitted between 2015 and 2021 to academic hospitals in Johannesburg, South Africa were retrospectively reviewed. Both the PLASMIC and the International Society of Thrombosis and Haemostasis (ISTH) DIC scores were calculated.
Patients with HIV-TTP had significantly (P < .001) increased schistocytes and features of hemolysis including elevated lactate dehydrogenase (LDH)/upper-limit-of-normal ratio (median of 9 (interquartile range [IQR] 5-12) vs 3 (IQR 2-5)) but unexpectedly lower fibrinogen (median 2.8 (IQR 2.2-3.4) vs 4 g/L (IQR 2.5-9.2)) and higher D-dimer (median 4.8 (IQR 2.4-8.1) vs 3.6 g/L (IQR 1.7-6.2)) levels vs the HIV-DIC cohort. Patients with HIV-DIC were more immunocompromised with frequent secondary infections, higher platelet and hemoglobin levels, more deranged coagulation parameters and less hemolysis. Overlap in scoring systems was however observed.
The laboratory parameter overlap between HIV-DIC and HIV-TTP might reflect a shared pathogenesis including endothelial dysfunction and inflammation and further research is required. Fibrinogen in DIC may be elevated as an acute phase reactant and D-dimers may reflect the extensive hemostatic activation in HIV-TTP. Inclusion of additional parameters in TMA scoring systems such the LDH/upper-limit-of-normal ratio, schistocytes count and wider access to ADAMTS-13 testing may enhance diagnostic accuracy and ensure appropriate utilization of plasma.
人类免疫缺陷病毒(HIV)感染患者存在血栓性微血管病(TMA)的风险,尤其是血栓性血小板减少性紫癜(TTP)和弥散性血管内凝血(DIC)。实验室结果存在重叠,导致诊断存在歧义。
回顾性分析了 2015 年至 2021 年期间南非约翰内斯堡两所学术医院收治的 71 例 HIV 相关 TTP(HIV-TTP)和 81 例并发 HIV 感染的 DIC(HIV-DIC)患者的常规实验室结果。计算了 PLASMIC 和国际血栓与止血学会(ISTH)DIC 评分。
HIV-TTP 患者的裂体细胞和溶血特征明显升高,包括乳酸脱氢酶(LDH)/正常上限比值升高(中位数为 9(四分位距 [IQR] 5-12)比 3(IQR 2-5)),但纤维蛋白原(中位数 2.8(IQR 2.2-3.4)比 4g/L(IQR 2.5-9.2))和 D-二聚体(中位数 4.8(IQR 2.4-8.1)比 3.6g/L(IQR 1.7-6.2))水平异常升高。HIV-DIC 患者免疫功能更差,经常发生继发感染,血小板和血红蛋白水平更高,凝血参数更紊乱,溶血程度更低。然而,评分系统存在重叠。
HIV-DIC 和 HIV-TTP 之间的实验室参数重叠可能反映了共同的发病机制,包括内皮功能障碍和炎症,需要进一步研究。DIC 中的纤维蛋白原可能作为急性期反应物升高,而 D-二聚体可能反映了 HIV-TTP 中广泛的止血激活。在 TMA 评分系统中纳入其他参数,如 LDH/正常上限比值、裂体细胞计数和更广泛地获得 ADAMTS-13 检测,可能会提高诊断准确性并确保适当利用血浆。