Wang Yan, Jiang Shuangshuang, Yang Jiasheng, Sun Ruilin
Guangdong Second Provincial General Hospital, China.
Respir Med Case Rep. 2022 Aug 13;39:101711. doi: 10.1016/j.rmcr.2022.101711. eCollection 2022.
UPVA (Unilateral pulmonary vein atresia) is the failure of connection between the common pulmonary vein and the left atrium. UPVA is a rare malformation of common pulmonary vein caused by embryonic development defects. Isolated UPVA is uncommon, the diagnosis commonly occurs during early childhood because of asthma, recurrent pneumonia or hemoptysis, but diagnosis in adults is unusual. Some patients can be asymptomatic until adulthood. In this report, we describe a case about UPVA presenting with recurrent hydrothorax in an adult. We gradually carried out routine diagnostic methods and eventually confirmed the rare UPVA according to the two common clinical manifestations of repeated pleural effusion and hilar soft tissue shadow.
单侧肺静脉闭锁（UPVA）是指肺总静脉与左心房之间连接中断。UPVA是一种由胚胎发育缺陷导致的罕见的肺总静脉畸形。孤立性UPVA并不常见，诊断通常在儿童早期因哮喘、反复肺炎或咯血而作出，但在成人中诊断并不常见。一些患者直到成年都可能无症状。在本报告中，我们描述了一例成年UPVA患者表现为反复胸腔积液的病例。我们逐步采用常规诊断方法，最终根据反复胸腔积液和肺门软组织影这两种常见临床表现确诊了这种罕见的UPVA。
