Sim Young Woo, Park Jongmin, Park Byunggeon, Lim Jae-Kwang, Shin Kyung Min, Kim Young-Seon
Taehan Yongsang Uihakhoe Chi. 2022 Mar;83(2):372-377. doi: 10.3348/jksr.2021.0033. Epub 2021 Oct 18.
Unilateral pulmonary vein atresia (PVA) is a rare congenital cardiovascular anomaly occurring after the common pulmonary vein fails to incorporate into the left atrium. It is most commonly diagnosed in childhood, and diagnosis after reaching adulthood is extremely rare. Dyspnea on exertion and hemoptysis are common clinical features in adult PVA patients, whereas lung parenchymal abnormalities are indirect signs of PVA, which can manifest as interstitial lung disease. Herein, we present the case of a 62-year-old female diagnosed with unilateral PVA presenting as unilateral interstitial lung disease and report the changes in her chest radiographs over 12 years.
单侧肺静脉闭锁（PVA）是一种罕见的先天性心血管异常，发生于共同肺静脉未能融入左心房之后。它最常在儿童期被诊断出来，成年后才被诊断的情况极为罕见。劳力性呼吸困难和咯血是成年PVA患者常见的临床特征，而肺实质异常是PVA的间接征象，可表现为间质性肺病。在此，我们报告一例62岁女性被诊断为单侧PVA并表现为单侧间质性肺病的病例，并报告其12年来胸部X线片的变化。
