极为晚期的肺转移：源自子宫的 PEComa。

Extremely late-onset pulmonary metastasis from uterine PEComa.

机构信息

Department of Radiological, Oncological and Pathological Sciences, Sapienza, University of Rome, Rome, Italy.

Department of Diagnostics and Public Health, University of Verona, Verona, Italy.

出版信息

Pathologica. 2022 Aug;114(4):312-315. doi: 10.32074/1591-951X-762. Epub 2022 Sep 8.

DOI:10.32074/1591-951X-762

PMID:36083244

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9624134/

Abstract

A 79-year-old woman underwent surgical resection of a peripheral, solitary, pulmonary lesion that was diagnosed as malignant PEComa. Her clinical history was positive for uterine leiomyosarcoma, excised 20 years before. Re-evaluation of the primary uterine lesion led to the final diagnosis of lung metastasis from uterine PEComa. While long latency between primary tumour and metastasis is a known and characteristic feature of PEComas, a 20-year interval is unprecedented in the literature.

摘要

一位 79 岁女性接受了外周性孤立性肺病变的手术切除，该病变被诊断为恶性的 PEComa。她的临床病史曾显示患有子宫平滑肌肉瘤，20 年前已切除。对原发性子宫病变的重新评估导致最终诊断为源自子宫的 PEComa 的肺转移。虽然原发性肿瘤和转移之间的长潜伏期是 PEComas 的一个已知且特征性的特征，但 20 年的间隔在文献中是前所未有的。