Balawender Krzysztof, Pliszka Anna, Możdżeñ Klaudia, Kłos Michał, Ogorzałek Anna, Boroñ Dariusz, Grabarek Beniamin O
Morphological Sciences Department of Human Anatomy, Institute of Medical Sciences, Medical College of Rzeszow University, Rzeszow, Poland.
Department of Histology, Cytophysiology and Embryology, Faculty of Medicine in Zabrze, University of Technology in Katowice, Poland.
Postepy Dermatol Alergol. 2022 Aug;39(4):739-743. doi: 10.5114/ada.2021.112465. Epub 2022 Jan 9.
The Rapunzel syndrome occurs when the trichobezoar (hair ball) extends beyond the small intestine and sometimes even into the colon, producing long, tail-like hair extensions.
To present cases of trichobezoars, an extremely rare human intestinal disease caused by the ingestion of hair (trichophagia).
In this retrospective study, we assessed the medical records of 2 patients diagnosed with Rapunzel syndrome admitted to Academic Clinical Hospital No. 2 in Rzeszow, Poland.
The first patient was a 15-year-old girl. The abdominal ultrasound examination revealed an abnormal, non-compressible structure with the approximate dimensions of 12 × 11 cm in the epigastrium, with a strong shadow obscuring the view. Gastroscopy was performed and a tumour sample was taken for histopathological examination, which confirmed the diagnosis of a trichobezoar. The patient's mother did not agree to her daughter's psychiatric treatment. The second patient was a 15-year-old girl who reported to the Emergency Room in critical condition due to dehydration and long-term emesis with symptoms of cachexia. Ileotomy with the removal of two trichobezoars with a diameter of about 5 cm and 7 cm was performed. The patient was discharged for treatment at the Mental Health Clinic for trichotillomania.
Trichobezoars give non-specific symptoms that may imitate other diseases for example tumours. Psychotherapy is the recommended treatment and follow-up visits are important in preventing relapses.
当毛粪石(毛发球)延伸至小肠以外,有时甚至进入结肠,产生长长的、尾状的毛发延伸时,就会发生长发公主综合征。
介绍毛粪石病例,这是一种由吞食毛发(拔毛癖)引起的极其罕见的人类肠道疾病。
在这项回顾性研究中,我们评估了波兰热舒夫第二学术临床医院收治的2例被诊断为长发公主综合征患者的病历。
首例患者为一名15岁女孩。腹部超声检查显示上腹部有一个异常的、不可压缩的结构,大小约为12×11厘米,有强烈阴影遮挡视线。进行了胃镜检查并采集肿瘤样本进行组织病理学检查,确诊为毛粪石。患者母亲不同意女儿接受精神科治疗。第二例患者是一名15岁女孩,因脱水和长期呕吐伴恶病质症状,病情危急被送往急诊室。进行了回肠切开术,取出了两个直径约5厘米和7厘米的毛粪石。患者出院后前往心理健康诊所接受拔毛癖治疗。
毛粪石会出现非特异性症状,可能会模仿其他疾病,例如肿瘤。推荐的治疗方法是心理治疗,随访对于预防复发很重要。