Obstetrics and Gynaecology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India.
Obstetrics and Gynaecology, All India Institute of Medical Sciences, Rishikesh, Uttarakhand, India
BMJ Case Rep. 2022 Sep 26;15(9):e251733. doi: 10.1136/bcr-2022-251733.
Primary ovarian leiomyosarcoma is a very uncommon and aggressive neoplasm. We presented a right-sided ovarian leiomyosarcoma in a woman in her late 40s. No case has been described in the literature till now of primary ovarian leiomyosarcoma in a woman with uterovaginal prolapse. A total abdominal hysterectomy with bilateral adnexectomy, metastasectomy, excision of large tumour deposit over small intestine followed by resection with ileo-ileal anastomosis and omentectomy was performed. The diagnosis was made based on morphology along with immunohistochemistry. The patient was given adjuvant chemotherapy during postoperative period. Due to rarity, there is a dearth of information on the clinical behaviour and best treatment options for these tumours. This case report highlighted the importance of clinical awareness and aimed to provide a baseline to guide clinical practice as well as future research.
原发性卵巢平滑肌肉瘤是一种非常罕见且侵袭性的肿瘤。我们报告了一例 40 多岁女性右侧卵巢平滑肌肉瘤。迄今为止,文献中尚未描述过患有阴道子宫脱垂的女性原发性卵巢平滑肌肉瘤。行全子宫切除术+双侧附件切除术、转移灶切除术、小肠表面巨大肿瘤病灶切除术,随后行回肠-回肠吻合术和网膜切除术。诊断基于形态学和免疫组织化学。术后给予辅助化疗。由于罕见,这些肿瘤的临床行为和最佳治疗方案的信息匮乏。本病例报告强调了临床意识的重要性,并旨在提供一个基准,以指导临床实践和未来的研究。