Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center and Fondazione Luigi Villa, Milan, Italy.
Padua University Hospital, Biomedical Sciences Department (DSB), Padua, Italy.
Haemophilia. 2023 Jan;29(1):11-20. doi: 10.1111/hae.14661. Epub 2022 Sep 27.
Haemophilia is a rare congenital bleeding disorder, and the most common manifestation is spontaneous bleeding in muscles and joints. Despite the benefits linked to recent and dramatic pharmacological advances at least in high income setting, many patients still develop musculoskeletal dysfunctions during their lifetime, which must be managed by physiotherapists in the frame of a multidisciplinary team. The aim of the scoping review is to map the available evidence by providing an overview on the past and present physiotherapy scenario in persons with haemophilia (PWH).
The review was conducted according to the guidelines of the PRISMA extension for scoping reviews. Scientific articles on physiotherapy and sport interventions for PWH published from 1960 up to September 2021 have been included. Search was conducted on the e-databases PubMed and PEDro without restrictions for the study design.
Sixty eight articles were included, 52 related to rehabilitation and preventive physiotherapy, 16 to sport. The results have been reported in chronological order and divided into two categories: (1) rehabilitation and preventive physiotherapy; (2) sport activities.
This is the first scoping review on physiotherapy in haemophilia, based on the existing evidence on this topic which allowed us to underline how the role of the physiotherapist changed over time. Historically this specialist did intervene only after an acute bleed or surgical operation, but now he has a pivotal role in the multidisciplinary team that acts to improve from birth the quality of life of the PWH. His activity is also closely intertwined with sport promotion and supervision.
血友病是一种罕见的先天性出血性疾病,最常见的表现是肌肉和关节自发性出血。尽管最近在高收入国家取得了显著的药物学进展,但至少在这些国家,许多患者在其一生中仍会出现肌肉骨骼功能障碍,这必须由理疗师在多学科团队的框架内进行管理。本综述的目的是通过概述血友病患者(PWH)过去和现在的理疗情况,来绘制现有证据图谱。
本综述按照 PRISMA 扩展的综述指南进行。纳入了从 1960 年到 2021 年 9 月发表的关于 PWH 理疗和运动干预的科学文章。在 e 数据库 PubMed 和 PEDro 上进行了无研究设计限制的检索。
共纳入 68 篇文章,其中 52 篇与康复和预防性理疗相关,16 篇与运动相关。结果按时间顺序报告,并分为两类:(1)康复和预防性理疗;(2)运动活动。
这是关于血友病理疗的首篇综述,基于该主题的现有证据,我们可以强调理疗师的角色是如何随着时间的推移而变化的。历史上,该专家仅在急性出血或手术干预后才进行干预,但现在他在多学科团队中发挥着关键作用,旨在从出生起就提高 PWH 的生活质量。他的活动也与促进和监督运动紧密交织在一起。