Gomes Joao Filipe, Vieira Ines, Mendes Jorge, Donaire David, Almeida Rui
Department of Internal Medicine, Coimbra Hospital and University Center, Coimbra, Portugal.
Department of Endocrinology Diabetes and Metabolism, Coimbra Hospital and University Center, Coimbra, Portugal.
J Coll Physicians Surg Pak. 2022 Oct;32(10):1353-1355. doi: 10.29271/jcpsp.2022.10.1353.
Leiomyosarcoma of the inferior vena cava is an extremely rare malignancy originating from the smooth muscle of the vessel wall, with only a few hundred cases reported in the literature. There are no clear guidelines for treatment, but surgical resection is currently the only curative option. Further research is needed to better understand the disease and guide its management. We report a case of a 39-year woman who presented to the emergency room with a four-day history of nonspecific abdominal pain, nausea and fever. An abdominal computed tomography revealed a mass in relation with the inferior vena cava and hepatic nodules. Histological examination proved it to be a leiomyosarcoma of inferior vena cava with liver metastases. Key Words: Leiomyosarcoma, Inferior vena cava, Sarcoma.
下腔静脉平滑肌肉瘤是一种极为罕见的恶性肿瘤，起源于血管壁的平滑肌，文献报道仅有数百例。目前尚无明确的治疗指南，但手术切除是目前唯一的治愈选择。需要进一步研究以更好地了解该疾病并指导其治疗。我们报告一例39岁女性患者，因非特异性腹痛、恶心和发热4天就诊于急诊室。腹部计算机断层扫描显示下腔静脉处有一肿块及肝脏结节。组织学检查证实为下腔静脉平滑肌肉瘤伴肝转移。关键词：平滑肌肉瘤；下腔静脉；肉瘤
