Savaş Bozbaş Şerife, Varan Birgül, Akçay Şule
Department of Chest Diseases, Baskent University, Ankara, Turkey.
Tuberk Toraks. 2012;60(3):254-7. doi: 10.5578/tt.2425.
Isolated pulmonary vein atresia without associated congenital malformation is a very rare condition in adults. It is associated with significant mortality and morbidity. Recurrent pulmonary infections, dyspnea on exertion and hemoptysis may be the presenting complaints. Owing to the limited number of patients with this condition there may be some difficulties in it's diagnosis and therapy. We report an adult case with this rare congenital malformation and discuss it's diagnosis and management options.
孤立性肺静脉闭锁且无相关先天性畸形在成人中是一种非常罕见的病症。它与显著的死亡率和发病率相关。反复肺部感染、劳力性呼吸困难和咯血可能是主要症状。由于患有这种病症的患者数量有限，其诊断和治疗可能存在一些困难。我们报告一例患有这种罕见先天性畸形的成年病例，并讨论其诊断和管理方案。
