Sivakumar Kothandam, Mumtaz Zeeshan Ahmed, Sagar Pramod
Department of Pediatric Cardiology, Institute of Cardio Vascular Diseases, Madras Medical Mission, Chennai, Tamil Nadu, India.
Ann Pediatr Cardiol. 2022 Mar-Apr;15(2):187-191. doi: 10.4103/apc.apc_2_22. Epub 2022 Aug 19.
Extreme pulmonary artery hypoplasia in cyanotic malformations precludes palliative surgeries. When aortopulmonary collaterals (APC) in such patients are also hypoplastic, their unifocalization to create a neopulmonary vasculature is also hampered. Stent angioplasty of the outflow or collateral arteries may reduce hypoxia but is challenging in tortuous and atretic tracts. Fusion imaging overlays anatomical data from computed tomography during adult structural interventions, but its use is not often reported in young children with complex cyanotic malformations. This report shows utility of fusion imaging in pulmonary atresia with extremely hypoplastic pulmonary arteries and stenotic APC to guide stenting of outflow tract and collaterals.
青紫型畸形中严重的肺动脉发育不全排除了姑息性手术的可能性。当此类患者的主肺动脉侧支(APC)也发育不全时,将它们整合为一体以构建新的肺血管系统也会受到阻碍。对流出道或侧支动脉进行支架血管成形术可能会减轻缺氧状况,但在迂曲和闭锁的血管路径中操作具有挑战性。融合成像在成人结构性干预期间叠加了来自计算机断层扫描的解剖数据,但在患有复杂青紫型畸形的幼儿中其应用情况鲜有报道。本报告展示了融合成像在肺动脉闭锁伴极重度肺动脉发育不全和狭窄性APC中的应用,以指导流出道和侧支的支架置入。