Liao Wen-Pen, Cheng Cheng-Kuo, Peng Pai-Huei
Department of Ophthalmology, Shin-Kong Wu Ho-Su Memorial Hospital, Taipei, Taiwan.
School of Medicine, Fu-Jen Catholic University, New Taipei, Taiwan.
Taiwan J Ophthalmol. 2022 Aug 18;12(3):360-363. doi: 10.4103/2211-5056.353125. eCollection 2022 Jul-Sep.
Peripapillary choroidal neovascularization (PPCNV), a rare presentation of optic nerve sheath meningioma (ONSM), is associated with various ocular pathologies. Herein, we report a case with characteristics of age-related macular degeneration, PPCNV, optic disc edema, and a retinal-choroidal venous collateral. In addition to the recognition of an orbital base ONSM, magnetic resonance imaging revealed a distended perioptic subarachnoid space with the accumulation of cerebrospinal fluid anterior to the tumor. On the basis of these clinical findings, we postulated the pathogenesis of PPCNV-associated ONSMs.
视乳头周围脉络膜新生血管形成(PPCNV)是视神经鞘膜瘤(ONSM)的一种罕见表现,与多种眼部病变相关。在此,我们报告一例具有年龄相关性黄斑变性、PPCNV、视盘水肿和视网膜 - 脉络膜静脉侧支特征的病例。除了识别眶底ONSM外,磁共振成像显示肿瘤前方视周蛛网膜下腔扩张并伴有脑脊液积聚。基于这些临床发现,我们推测了与PPCNV相关的ONSM的发病机制。