Yusuf Ali Abdullahi, Biyikli Ahmet, Abdi Abdishakur Mohamed, Guler Ilkay
Department of Pediatric Surgery, Somalia Turkish Training and Research Hospital, Mogadishu, Somalia.
General Directorate of Public Hospitals, Ministry of Health of Republic of Turkiye, Ankara, Turkey.
Int Med Case Rep J. 2022 Oct 28;15:605-609. doi: 10.2147/IMCRJ.S385808. eCollection 2022.
The infantile intestinal obstruction associated with situs inversus totalis and polysplenia is extremely rare, with only a few cases reported in the literature. Furthermore, the management of this association is complicated. We report a case of a 2-month-old boy with intestinal obstruction due to malrotation and volvulus with thin translucent omentum sac encasing the small intestine associated with situs inversus totalis, polysplenia, and pulmonary hypertension. To the best of our knowledge, this is the first case of situs inversus totalis with polysplenia, pulmonary hypertension, and intestinal obstruction due to malrotation and volvulus with thin translucent omentum sac encasing the small intestine.
与全内脏转位和多脾畸形相关的婴儿肠梗阻极为罕见，文献中仅报道了少数病例。此外，这种联合病症的治疗很复杂。我们报告了一例2个月大的男孩，因肠旋转不良和肠扭转导致肠梗阻，伴有包裹小肠的薄而半透明的网膜囊，同时合并全内脏转位、多脾畸形和肺动脉高压。据我们所知，这是首例全内脏转位合并多脾畸形、肺动脉高压，且因肠旋转不良和肠扭转伴有包裹小肠的薄而半透明网膜囊导致肠梗阻的病例。
