Alshaikh Murtadha A, Al Ghadeer Hussain A, Alabad Hamed, Almohsin Madinah, Al Ali Roqaia A
Pediatric Department, Maternity and Children Hospital, Al-Ahsa, SAU.
Urology Department, Defense Force Hospital, Manama, BHR.
Cureus. 2021 Sep 6;13(9):e17764. doi: 10.7759/cureus.17764. eCollection 2021 Sep.
Situs inversus totalis is the mirror image transposition of the abdominal-thoracic viscera. Approximately one in every 5,000 to 20,000 live births has situs inversus totalis. Most commonly, it is found incidentally and is asymptomatic. A number of malformations, including cardiac, splenic, and gastrointestinal, have been associated with this condition. Coexistence with duodenal atresia is extremely rare, reported in fewer than 30 cases worldwide and one case in Saudi Arabia. We report a preterm neonate who presented with bilious vomiting. Diagnosis of situs inversus totalis with duodenal atresia type III was established and other anomalies were ruled out. The patient was managed surgically by duodenal-duodenostomy and Ladd's procedure. The report emphasizes the importance of identifying this condition and recognizing the "mirror anatomy" before carrying out an operation. Once the diagnosis is confirmed, surgical intervention must be performed as soon as possible to prevent complications.
完全性内脏反位是胸腹内脏的镜像转位。每5000至20000例活产儿中约有1例患有完全性内脏反位。最常见的情况是偶然发现且无症状。包括心脏、脾脏和胃肠道在内的一些畸形与这种情况有关。与十二指肠闭锁并存极为罕见，全球报告少于30例，沙特阿拉伯有1例。我们报告1例出现胆汁性呕吐的早产儿。确诊为完全性内脏反位合并III型十二指肠闭锁，排除了其他异常。患者接受了十二指肠十二指肠吻合术和Ladd手术。该报告强调了在手术前识别这种情况并认识“镜像解剖结构”的重要性。一旦确诊，必须尽快进行手术干预以预防并发症。
