Rocamora Salort Sandra, Ruiz González Eladio, Cano Sánchez Ana, Fernández Tudela Belén
Division of Pediatric Cardiology, Department of Pediatrics, University Hospital of the Canary Islands, Carretera de La Cuesta s/n, 38320 La Laguna, Tenerife, Canary Islands, Spain.
Division of Pediatric Cardiology, Department of Pediatrics, La Fe University and Polytechnic Hospital, 46026 Valencia, Spain.
Eur Heart J Case Rep. 2022 Oct 15;6(11):ytac415. doi: 10.1093/ehjcr/ytac415. eCollection 2022 Nov.
Total anomalous pulmonary venous return is a rare cyanotic congenital heart disease in which pulmonary veins connect to the systemic veins, right atrium, or coronary sinus. Given its variability, it is essential to define the pathway and drainage site.
We describe a 3-day-old patient with total anomalous pulmonary venous return, in which the four pulmonary veins drained into a common vertical vein that had a double connection at the cardiac (coronary sinus) and infracardiac (portal vein) levels. The echocardiographic diagnosis was confirmed by computed tomography scan. At 1.5 months, she underwent surgery by anastomosis of the venous collector with the left atrium, unroof of the coronary sinus, and clousure of its communication with right atrium. The vertical vein was ligated. There were no complications after 1 year of follow-up.
This is an unusual anatomy that has not been described in the literature. In this article, we discuss the embryological origin. Furthermore, we highlight the importance of an accurate diagnosis of the venous pathway and its impact on surgical planning and patient prognosis.
完全性肺静脉异位回流是一种罕见的青紫型先天性心脏病，其肺静脉与体静脉、右心房或冠状窦相连。鉴于其变异性，明确其路径和引流部位至关重要。
我们描述了一名3日龄完全性肺静脉异位回流患者，其四条肺静脉汇入一条共同的垂直静脉，该垂直静脉在心脏（冠状窦）和心下（门静脉）水平有双重连接。超声心动图诊断经计算机断层扫描证实。1.5个月时，她接受了手术，将静脉收集器与左心房吻合，冠状窦开窗，并封闭其与右心房的交通。结扎垂直静脉。随访1年后无并发症。
这是一种文献中未描述过的不寻常解剖结构。在本文中，我们讨论了其胚胎学起源。此外，我们强调了准确诊断静脉路径及其对手术规划和患者预后的影响的重要性。
