Faculty of Medicine, Tartous University, Tartus, Syrian Arab Republic.
MSc Global Public Health Nutrition, School of Life Sciences, University of Westminster, London, UK.
BMC Urol. 2022 Nov 10;22(1):179. doi: 10.1186/s12894-022-01137-x.
Situs inversus totalis is a very rare congenital anatomical variation, in which all thoracic and abdominal organs are right-left inverted. This condition is associated with an increased risk of organ malformations including ectopic kidney, which is a very rare combination.
A 56-year-old male presented with colicky left iliac pain associated with nausea, vomiting, and irritative lower urinary symptoms. The patient has a medical history of recurrent lower urinary infections and a family history of situs inversus totalis. Radiological images demonstrated dextrocardia, situs inversus totalis of all the abdominal organs, and an ectopic pelvic kidney on the left side, with 4 stones inside it. Left nephrectomy was performed due to extensive renal damage. At discharge and during follow-up, the patient's condition was satisfactory and stable.
The ectopic kidney may present diagnostic and therapeutic challenges when associated with situs inversus.
全内脏反位是一种非常罕见的先天性解剖变异,所有的胸部和腹部器官均左右反转。这种情况与器官畸形的风险增加有关,包括异位肾,这是一种非常罕见的组合。
一名 56 岁男性因左侧髂窝绞痛伴恶心、呕吐和刺激性下尿路症状就诊。患者有复发性下尿路感染病史和全内脏反位家族史。影像学图像显示右位心、所有腹部器官全内脏反位和左侧异位盆腔肾,其内有 4 颗结石。由于广泛的肾损伤,行左肾切除术。出院和随访期间,患者情况良好且稳定。
当异位肾与全内脏反位相关时,可能会带来诊断和治疗方面的挑战。