Neurosurgery Department, Garrahan Hospital, Buenos Aires, Argentina.
Childs Nerv Syst. 2023 Apr;39(4):1097-1100. doi: 10.1007/s00381-022-05753-8. Epub 2022 Nov 17.
Choroidal fissure cysts (CFC) are usually an incidental finding on imaging and lead to morbidity only in rare cases. The aim of this study was to present the case of a patient with a giant CFC and its treatment.
The patient was a male infant of 9 days of life that presented with symptoms of intracranial hypertension. A CFC measuring 56 × 70 × 86 mm was diagnosed. Endoscopic fenestration of the cyst was performed; however, the communication closed thereafter. A reservoir catheter was inserted, which subsequently became infected and was then replaced by a ventriculoperitoneal shunt.
The choroidal fissure is a C-shaped cleft located between the fornix and the thalamus separated from the temporal horn by the layer of tela choroidea. The pathophysiology of CFC is still unclear. In our case, initial endoscopic treatment was decided on to avoid shunt-related complications. Currently, there are no guidelines for the best surgical treatment for CFC.
We describe an atypical case of CFC and analyze the surgical treatment performed. Although endoscopic treatment is recommended for CFC, currently no guidelines exist regarding the best management of the entity.
脉络膜裂囊肿(CFC)通常在影像学检查中是偶然发现的,只有在极少数情况下才会引起发病。本研究的目的是报告一例巨大脉络膜裂囊肿及其治疗的病例。
患者为男性,9 天大,有颅内压增高的症状。诊断为一个 56×70×86mm 的脉络膜裂囊肿。对囊肿进行了内镜开窗术,但此后沟通关闭。插入了一个储液囊导管,但后来导管感染,随后更换为脑室腹腔分流术。
脉络膜裂是一个 C 形裂隙,位于穹窿和丘脑之间,由脉络膜层与颞角隔开。CFC 的病理生理学仍然不清楚。在我们的病例中,最初决定采用内镜治疗以避免分流相关并发症。目前,对于 CFC 的最佳手术治疗尚无指南。
我们描述了一个 CFC 的非典型病例,并分析了所进行的手术治疗。虽然内镜治疗被推荐用于 CFC,但目前对于该实体的最佳管理尚无指南。