Atamari-Anahui Noé, Domínguez-Rojas Jesús, Ruiz-Solsol Luis, López-Turpo Maryori, Castillo-Delgadillo Amarilis, Quiñonez Saif David, Campano Cornejo J William
Instituto Nacional de Salud del Niño-Breña. Lima, Perú; Universidad San Ignacio de Loyola, Vicerrectorado de Investigación, Unidad de Investigación para la Generación y Síntesis de Evidencias en Salud. Lima, Perú.
Instituto Nacional de Salud del Niño-Breña. Lima, Perú; Universidad Nacional Mayor de San Marcos. Lima, Perú.
Rev Gastroenterol Peru. 2022 Apr-Jun;42(2):131-135.
Budd-Chiari syndrome is caused by an obstruction of blood flow to the liver. Published cases of the antiphospholipid syndrome associated with BCS are limited in the pediatric population. We report a 15-year-old adolescent who presented with fever, ascites, and hepatosplenomegaly. Hepatic Doppler ultrasound revealed no flow in the right and middle hepatic veins and in the inferior vena cava. Abdominal tomography revealed extensive thrombosis of the inferior vena cava. During hospitalization, she was diagnosed with antiphospholipid syndrome and systemic lupus erythematosus. She was given treatment with unfractionated heparin, low molecular weight heparin, and anticoagulants. Budd-Chiari syndrome secondary to the antiphospholipid syndrome is a life-threatening disease. Timely diagnosis and treatment improve the quality of life of the patient.
布加综合征是由肝脏血流受阻引起的。小儿人群中与布加综合征相关的抗磷脂综合征的已发表病例有限。我们报告一名15岁青少年，表现为发热、腹水和肝脾肿大。肝脏多普勒超声显示右肝静脉、中肝静脉及下腔静脉无血流信号。腹部断层扫描显示下腔静脉广泛血栓形成。住院期间，她被诊断为抗磷脂综合征和系统性红斑狼疮。给予她普通肝素、低分子肝素和抗凝剂治疗。抗磷脂综合征继发的布加综合征是一种危及生命的疾病。及时诊断和治疗可提高患者的生活质量。
