Clements B S, Warner J O
Department of Paediatrics, Brompton Hospital, London.
Thorax. 1987 Jun;42(6):417-9. doi: 10.1136/thx.42.6.417.
Three cases of a congenitally misplaced segment of lung are described. In one case the abnormal segment was identified at thoracotomy; it extended from an origin in the right upper lobe across the midline into the left hemithorax. The remaining two patients, with identical radiographic features, were identified in a review of 24 cases of bronchovascular malformation. In all three patients the crossover segment was associated with a variant of the scimitar syndrome: right lung hypoplasia with dextrocardia, aberrant systemic arterial supply to the right lower lobe, and anomalous venous drainage of the whole of the right lung, and in two patients with eventration of the right diaphragm.
本文描述了三例先天性肺段异位的病例。其中一例在开胸手术中发现异常肺段；它起源于右上叶，穿过中线延伸至左半胸。另外两名患者具有相同的影像学特征，是在对24例支气管血管畸形病例的回顾中发现的。在所有三名患者中，交叉肺段均与弯刀综合征的一种变体相关：右肺发育不全伴右位心、右下叶有异常体动脉供血以及整个右肺有异常静脉引流，且两名患者伴有右侧膈膨升。
