Department of Oral and Maxillofacial Pathology, Vivekanandha Dental College for Women, Tamil Nadu, India.
Department of Oral and Maxillofacial Pathology, KSR Institute of Dental Science and Research, Tamil Nadu, India.
Indian J Dent Res. 2022 Jul-Sep;33(3):323-331. doi: 10.4103/ijdr.ijdr_456_22.
Ameloblastoma is a benign, locally aggressive neoplasm that needs extensive surgical resection. The goal of this article is to obtain an in-depth review of benign ameloblastomas to determine the available level of evidence and the possible benefit of targeted therapeutics for the treatment of ameloblastoma and BRAF V600E mutation in ameloblastoma. An electronic literature search was conducted according to PRISMA guidelines in PubMed/MEDLINE, EBSCO, and Web of Science for eligible studies published between 1975 and 2021. The systematic review is registered with INPLASY (INPLASY202260018). The review included 2 case series and 17 case reports. The histopathological type, anatomic location, expression of BRAF mutation, additional mutations, and molecular-targeted therapies of the 19 reviewed articles were summarized and tabulated. Interestingly, the majority of the primary site of ameloblastoma was located in the mandible (80.9%) compared to the maxilla (17%). The tumour size was reported in nine of the included studies. Most of the included studies in the review exhibited ameloblastoma with BRAF V600E mutations and responded to molecular-targeted therapies. Molecular therapies employing BRAF and/or MEK inhibitors in ameloblastoma with BRAF V600E mutations proved to be an appropriate treatment based on the limited available evidence. It is essential further to deepen our understanding at the clinical and molecular level to enhance the precision of management of ameloblastoma.
成釉细胞瘤是一种良性、局部侵袭性肿瘤,需要广泛的手术切除。本文的目的是深入研究良性成釉细胞瘤,以确定现有的证据水平和针对成釉细胞瘤和成釉细胞瘤中 BRAF V600E 突变的靶向治疗的可能益处。根据 PRISMA 指南,在 PubMed/MEDLINE、EBSCO 和 Web of Science 中进行了电子文献检索,以获取 1975 年至 2021 年期间发表的合格研究。系统评价在 INPLASY(INPLASY202260018)中注册。该综述包括 2 个病例系列和 17 个病例报告。总结和制表了 19 篇综述文章的组织病理学类型、解剖位置、BRAF 突变表达、其他突变和分子靶向治疗。有趣的是,成釉细胞瘤的大部分原发性部位位于下颌骨(80.9%),而上颌骨(17%)。在纳入的 9 项研究中报告了肿瘤大小。综述中纳入的大多数研究显示具有 BRAF V600E 突变的成釉细胞瘤,并对分子靶向治疗有反应。在具有 BRAF V600E 突变的成釉细胞瘤中使用 BRAF 和/或 MEK 抑制剂的分子治疗已被证明是一种合适的治疗方法,这是基于有限的可用证据。进一步深入了解临床和分子水平对于提高成釉细胞瘤的管理精度至关重要。