Marwick T H, Woodhouse S P, Birchley I N, Strong R W
Department of Cardiology, Princess Alexandra Hospital, Woolloongabba, Queensland, Australia.
Chest. 1987 Nov;92(5):954-6. doi: 10.1378/chest.92.5.954.
Aortic dissection uncommonly occurs in multiple family members, and this association is most commonly seen in kindreds with Marfan's syndrome. There is increasing evidence that such connective tissue disturbances may not always appear in their complete phenotypic pattern. This report describes two siblings with aortic dissection. It is proposed that this suggests underlying connective tissue disease and warrants investigation of close relatives.
主动脉夹层在多个家庭成员中罕见发生，这种关联最常见于患有马方综合征的家族中。越来越多的证据表明，这种结缔组织紊乱可能并不总是以其完整的表型模式出现。本报告描述了两名患有主动脉夹层的兄弟姐妹。有人提出，这表明存在潜在的结缔组织疾病，值得对其近亲进行调查。
