Teien D, Finley J P, Murphy D A, Lacson A, Longhi J, Gillis D A
Department of Cardiology, Izaak Walton Killam Hospital for Children, Dalhousie University, Halifax, Canada.
Acta Paediatr Scand. 1991 Dec;80(12):1246-9. doi: 10.1111/j.1651-2227.1991.tb11818.x.
Dissection of the aorta is very rare in children, but classically occurs in the presence of Marfan syndrome or other connective tissue disorder. We present a case of spontaneous dissection in a 12-year-old boy whose half brother has an idiopathic dilated aorta and whose mother has also required surgery for dissection of a dilated aorta. No features of connective tissue disorder were present in any family member.
主动脉夹层在儿童中非常罕见，但典型情况下发生于患有马凡综合征或其他结缔组织疾病的患者。我们报告一例12岁男孩自发性主动脉夹层病例，其同父异母的哥哥患有特发性主动脉扩张，其母亲也曾因主动脉扩张夹层而接受手术。家族成员中均无结缔组织疾病的特征表现。
