Witt P, Thomas E
J Natl Med Assoc. 1987 Sep;79(9):993-4, 996.
Esophageal involvement in scleroderma is generally confined to the body, manifested manometrically as impaired motility and decreased lower esophageal sphincter tone. Pharyngeal dysfunction has not been recognized. This is a report of a patient with the rare combination of scleroderma and ankylosing spondylitis, whose presenting complaint was transfer dysphagia due to impaired relaxation of the upper esophageal spincter as a result of tight overlying cervical skin, or sclerodermatous involvement of the sphincter itself.
硬皮病累及食管通常局限于食管体部,测压表现为动力障碍和食管下括约肌张力降低。咽部功能障碍尚未得到认识。本文报告1例罕见的硬皮病合并强直性脊柱炎患者,其主要症状是由于颈部上方皮肤紧绷导致食管上括约肌松弛受损,或括约肌本身硬皮病性受累而出现的转送性吞咽困难。