Hoffman H J, Neill J, Crone K R, Hendrick E B, Humphreys R P
Division of Neurosurgery, University of Toronto, Ontario.
Neurosurgery. 1987 Sep;21(3):347-51. doi: 10.1227/00006123-198709000-00012.
Syringomyelia, once regarded as a degenerative disease of adults, is now recognized to be a disorder usually associated with the Chiari malformation and occurring in patients of all ages. We have reviewed 47 patients with syringomyelia treated on the Neurosurgical Service at the Hospital for Sick Children during the years 1977 to 1985. Twelve of these patients had a Chiari I malformation, 30 had a Chiari II malformation, and 5 had an acquired Chiari malformation. Thirty-one of these patients were treated by decompression of the Chiari malformation and plugging of the obex, 5 were treated by a simple posterior fossa decompression, 9 were treated by shunting of the syringomyelic cavity, and 2 were treated by a combined decompression of the posterior fossa and shunting of the syrinx. The Gardner procedure (decompression of the Chiari malformation and plugging of the obex) was the procedure most commonly used in managing our group of patients and resulted in improvement in over 70% of patients.
脊髓空洞症，曾被视为成人的一种退行性疾病，现在被认为是一种通常与Chiari畸形相关且在各年龄段患者中均会出现的病症。我们回顾了1977年至1985年期间在病童医院神经外科接受治疗的47例脊髓空洞症患者。其中12例患有Chiari I畸形，30例患有Chiari II畸形，5例患有后天性Chiari畸形。这些患者中有31例接受了Chiari畸形减压及闩部填塞治疗，5例接受了单纯后颅窝减压治疗，9例接受了脊髓空洞腔分流治疗，2例接受了后颅窝减压与脊髓空洞分流联合治疗。Gardner手术（Chiari畸形减压及闩部填塞）是我们治疗这组患者最常用的手术方法，超过70%的患者病情得到改善。
